NHLBI Logo Mammalian Metabolic Enzyme Database

Comprehensive Mammalian Metabolic Enzyme Database. This searchable, sortable database lists official gene symbols for major mammalian metabolic enzymes. To identify descriptors, these metabolic enzymes were mapped to NCBI's BioSystems pathways and standard metabolic charts from Roche and Sigma-Aldrich (Sigma). To create a more comprehensive list, we added gene symbols from the MitoCarta database of mitochondrial proteins that were not included in our original list.

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This database was created by Callan Corcoran, Cameron Grady, Jaya Parulekar, Trairak Pisitkun, and Mark Knepper in the Epithelial Systems Biology Laboratory (ESBL) of the National Heart, Lung, and Blood Institute (NHLBI). Please report any additions or corrections to the Knepper Lab via knep@helix.nih.gov. If you use this database in any published work, please cite the associated article as follows: Corcoran CC, Grady CR, Parulekar J, Pisitkun T, Knepper MA. From 20th century metabolic wall charts to 21st century systems biology: database of mammalian metabolic enzymes. Am J Physiol Renal Physiol. 2017 Mar 1;312(3):F533-F542. PMID: 27974320.

Gene Symbol Annotation BioSystems Pathways Roche Chart Sector Roche Chart Subsector Sigma Chart Substrate Sigma Chart General Term Sigma MiniMap Term
Aadac arylacetamide deacetylase 13184050 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Aadat kynurenine/alpha-aminoadipate aminotransferase, mitochondrial 568954777 Amino Acid Metabolism: Lysine; Nucleotide Metabolism: NAD, NADP; Lysine Metabolism; Amino Acids; Amino acids;
Aars2 alanine--tRNA ligase, mitochondrial * 1039753383
Aasdh acyl-CoA synthetase family member 4-like isoform X6 30348962 Amino Acid Metabolism: Lysine; Lysine Metabolism; Amino Acids; Amino acids;
Aass alpha-aminoadipic semialdehyde synthase, mitochondrial precursor 31980703 Amino Acid Metabolism: Lysine; Lysine Metabolism; Amino Acids; Amino acids;
Abat 4-aminobutyrate aminotransferase, mitochondrial 283483966 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Asparate Group of Amino Acids; Glutamate Decarboxylation Pathway; Amino Acids; Amino acids; Pyrimidine Metabolism;
Abhd1 abhydrolase domain-containing protein 1 15011864 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd10 mycophenolic acid acyl-glucuronide esterase, mitochondrial precursor 440918693 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd11 abhydrolase domain containing 11 1039772435 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd12 monoacylglycerol lipase ABHD12 159110817 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd12b abhydrolase domain-containing protein 12B 303324606 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd13 abhydrolase domain-containing protein 13 299473802 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd14a alpha/beta hydrolase domain-containing protein 14A precursor 1039794057 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd14b alpha/beta hydrolase domain-containing protein 14B 1039794594 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd15 abhydrolase domain-containing protein 15 precursor 147902337 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd16a abhydrolase domain-containing protein 16A 30519896 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd16b abhydrolase domain-containing protein 16B 34147236 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd17a alpha/beta hydrolase domain-containing protein 17A precursor 1039732717 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd17b alpha/beta hydrolase domain-containing protein 17B precursor 755563143 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd17c abhydrolase domain-containing protein FAM108C1 158186616 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd2 abhydrolase domain-containing protein 2 40254377 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd3 abhydrolase domain-containing protein 3 755560327 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd4 abhydrolase domain-containing protein 4 568986337 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd5 1-acylglycerol-3-phosphate O-acyltransferase ABHD5 13385690 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd6 monoacylglycerol lipase ABHD6 1062594015 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Abhd8 abhydrolase domain-containing protein 8 257153457 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Acaa1a 3-ketoacyl-CoA thiolase A, peroxisomal 568963429 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Fatty Acids; Branched Chain Amino Acids; Fatty Acid Oxidation; Amino Acids; Amino acids; Lipid degradation; Lipid Metabolism;
Acaa1b 3-ketoacyl-CoA thiolase B, peroxisomal precursor 755531999 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Fatty Acids; Branched Chain Amino Acids; Fatty Acid Oxidation; Amino Acids; Amino acids; Lipid degradation; Lipid Metabolism;
Acaa2 3-ketoacyl-CoA thiolase, mitochondrial 29126205 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Fatty Acids; Branched Chain Amino Acids; Fatty Acid Oxidation; Amino Acids; Amino acids; Lipid degradation; Lipid Metabolism;
Acaca acetyl-CoA carboxylase 1 755537049 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Lipid Metabolism: Fatty Acids; Fatty Acid Synthesis; Sulfur Metabolism; Lipid Metabolism;
Acacb acetyl-CoA carboxylase 2 568936761 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Lipid Metabolism: Fatty Acids; Fatty Acid Synthesis; Sulfur Metabolism; Lipid Metabolism;
Acad10 acyl-CoA dehydrogenase family member 10* 156255157
Acad11 acyl-CoA dehydrogenase family member 11* 74271799
Acad12 acyl-Coenzyme A dehydrogenase family, member 10-like * 755513797
Acad8 isobutyryl-CoA dehydrogenase, mitochondrial * 1039793920
Acad9 acyl-CoA dehydrogenase family member 9, mitochondrial* 100817933
Acadl long-chain specific acyl-CoA dehydrogenase, mitochondrial precursor 31982520 Amino Acids; Amino acids; Lipid degradation; Lipid Metabolism;
Acadm medium-chain specific acyl-CoA dehydrogenase, mitochondrial precursor 6680618 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Lipid Metabolism: Fatty Acids; Branched Chain Amino Acids; Fatty Acid Oxidation; Sulfur Metabolism; Amino Acids; Amino acids; Lipid degradation; Lipid Metabolism;
Acads short-chain specific acyl-CoA dehydrogenase, mitochondrial precursor 31982522 Lipids; Lipid degradation; Lipid Metabolism;
Acadsb short/branched chain specific acyl-CoA dehydrogenase, mitochondrial* 17647119
Acadvl very long-chain specific acyl-CoA dehydrogenase, mitochondrial precursor 23956084 Amino Acids; Amino acids; Lipid degradation; Lipid Metabolism;
Acat1 acetyl-CoA acetyltransferase, mitochondrial precursor 21450129 Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Ketone Bodies; Zoosterols; Lipids; Lipid degradation; Lipid Metabolism;
Acat2 acetyl-CoA acetyltransferase, cytosolic 148747461 Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Ketone Bodies; Zoosterols; Lipids; Lipid degradation; Lipid Metabolism;
Acat3 acetyl-Coenzyme A acetyltransferase 3 110625948 Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Ketone Bodies; Zoosterols; Lipids; Lipid degradation; Lipid Metabolism;
Acer1 alkaline ceramidase 1 28376625 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Acer2 alkaline ceramidase 2 755506368 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Acer3 alkaline ceramidase 3 84794581 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Ache acetylcholinesterase precursor 1039770231 Lipid Metabolism: Glyco- and Phospholipids;
Acly ATP-citrate synthase isoform 1 313151222 Citrate and Glyoxalate Cycle; Glyoxylate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Anaplerotic Reactions of the TCA Cycle; Lipid Metabolism;
Acmsd 2-amino-3-carboxymuconate-6-semialdehyde decarboxylase 74315894 Nucleotide Metabolism: NAD, NADP; Amino Acids; Aromatic amino acids;
Aco1 cytoplasmic aconitate hydratase 110347487 Citrate and Glyoxalate Cycle; Citrate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle;
Aco2 aconitate hydratase, mitochondrial precursor 18079339 Citrate and Glyoxalate Cycle; Citrate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle;
Acot1 acyl-coenzyme A thioesterase 1 6753550 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipids; Lipid biosynthesis;
Acot10 acyl-coenzyme A thioesterase 10, mitochondrial precursor 154426268 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipids; Lipid biosynthesis;
Acot11 acyl-CoA thioesterase 11 755508325 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipids; Lipid biosynthesis;
Acot12 acyl-coenzyme A thioesterase 12 568983708 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipids; Lipid biosynthesis;
Acot13 acyl-coenzyme A thioesterase 13 13385260 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipids; Lipid biosynthesis;
Acot2 acyl-coenzyme A thioesterase 2, mitochondrial 238624114 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipids; Lipid biosynthesis;
Acot3 acyl-CoA thioesterase 3 568978890 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipids; Lipid biosynthesis;
Acot4 acyl-coenzyme A thioesterase 4 269308227 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipids; Lipid biosynthesis;
Acot5 acyl-coenzyme A thioesterase 5 1039740153 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipids; Lipid biosynthesis;
Acot6 acyl-coenzyme A thioesterase 6 110626167 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipids; Lipid biosynthesis;
Acot7 cytosolic acyl coenzyme A thioester hydrolase isoform 1 568931880 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipids; Lipid biosynthesis;
Acot8 acyl-coenzyme A thioesterase 8 755498808 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipids; Lipid biosynthesis;
Acot9 acyl-coenzyme A thioesterase 9, mitochondrial 922960017 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipids; Lipid biosynthesis;
Acox1 peroxisomal acyl-coenzyme A oxidase 1 * 429484484
Acox2 peroxisomal acyl-coenzyme A oxidase 2 * 568985621
Acox3 peroxisomal acyl-coenzyme A oxidase 3 * 1039772943
Acp1 low molecular weight phosphotyrosine protein phosphatase * 159032062
Acp2 lysosomal acid phosphatase * 755498552
Acp5 tartrate-resistant acid phosphatase type 5 * 156151433
Acp6 lysophosphatidic acid phosphatase type 6 * 66773165
Acp7 acid phosphatase type 7 * 568944672
Acpp prostatic acid phosphatase long isoform precursor 46575784 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Acsbg1 long-chain-fatty-acid--CoA ligase ACSBG1 568962373 Carbohydrates; Lipid biosynthesis; Lipid Metabolism;
Acsbg2 long-chain-fatty-acid--CoA ligase ACSBG2 755556892 Carbohydrates; Lipid biosynthesis; Lipid Metabolism;
Acsf2 acyl-CoA synthetase family member 2, mitochondrial * 24418933
Acsf3 acyl-CoA synthetase family member 3, mitochondrial * 113199775
Acsl1 long-chain-fatty-acid--CoA ligase 1 31560705 Carbohydrates; Lipid biosynthesis; Lipid Metabolism;
Acsl2 long-chain-fatty-acid--CoA ligase 1 338817850 Carbohydrates; Lipid biosynthesis; Lipid Metabolism;
Acsl3 long-chain-fatty-acid--CoA ligase 3 209977076 Carbohydrates; Lipid biosynthesis; Lipid Metabolism;
Acsl4 long-chain-fatty-acid--CoA ligase 4 75992925 Carbohydrates; Lipid biosynthesis; Lipid Metabolism;
Acsl5 long-chain-fatty-acid--CoA ligase 5 58218988 Carbohydrates; Lipid biosynthesis; Lipid Metabolism;
Acsl6 long-chain-fatty-acid--CoA ligase 6 75992917 Carbohydrates; Lipid biosynthesis; Lipid Metabolism;
Acsm1 acyl-coenzyme A synthetase ACSM1, mitochondrial * 568949358
Acsm2 acyl-coenzyme A synthetase ACSM2, mitochondrial * 295789127
Acsm3 acyl-coenzyme A synthetase ACSM3, mitochondrial* 85810992
Acsm4 acyl-coenzyme A synthetase ACSM4, mitochondrial * 30410742
Acsm5 acyl-coenzyme A synthetase ACSM5, mitochondrial * 755522749
Acss1 acetyl-coenzyme A synthetase 2-like, mitochondrial 18034773 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Sulfur Metabolism;
Acss2 acetyl-coenzyme A synthetase, cytoplasmic 1039761503 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Sulfur Metabolism; Carbohydrates; Lipid biosynthesis; Lipid Metabolism;
Acss3 acyl-CoA synthetase short-chain family member 3, mitochondrial isoform X3 218563743 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Sulfur Metabolism;
Acyp1 acylphosphatase-1* 13384810
Acyp2 acylphosphatase-2 * 1039738541
Ada adenosine deaminase 440309866 Nucleotide Metabolism: Purines; Purine Metabolism;
Adcy1 adenylate cyclase type 1 61888832 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Purines and Pyrimidines; Purines;
Adcy10 adenylate cyclase type 10 1039729131 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Purines and Pyrimidines; Purines;
Adcy2 adenylate cyclase type 2 124244092 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Purines and Pyrimidines; Purines;
Adcy3 adenylate cyclase type 3 568977427 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Purines and Pyrimidines; Purines;
Adcy4 adenylate cyclase type 4 568986247 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Purines and Pyrimidines; Purines;
Adcy5 adenylate cyclase type 5 148747309 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Purines and Pyrimidines; Purines;
Adcy6 adenylate cyclase type 6 isoform 1 1039747994 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Purines and Pyrimidines; Purines;
Adcy7 adenylate cyclase type 7 157951653 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Purines and Pyrimidines; Purines;
Adcy8 adenylate cyclase type 8 1062594090 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Purines and Pyrimidines; Purines;
Adcy9 adenylate cyclase type 9 isoform 2 755553083 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Purines and Pyrimidines; Purines;
Adh1 alcohol dehydrogenase 1 6724311 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Steroid Metabolism: Cholesterol Synthesis; Anaplerotic Reactions; Zoosterols; Amino Acids; Amino acids;
Adh1a alcohol dehydrogenase 1A 113390 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Steroid Metabolism: Cholesterol Synthesis; Anaplerotic Reactions; Zoosterols; Amino Acids; Amino acids;
Adh1b alcohol dehydrogenase 1B isoform 2 113394 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Steroid Metabolism: Cholesterol Synthesis; Anaplerotic Reactions; Zoosterols; Amino Acids; Amino acids;
Adh1c alcohol dehydrogenase 1C 113398 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Steroid Metabolism: Cholesterol Synthesis; Anaplerotic Reactions; Zoosterols; Amino Acids; Amino acids;
Adh3 alcohol dehydrogenase 1C 113398 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Steroid Metabolism: Cholesterol Synthesis; Anaplerotic Reactions; Zoosterols; Amino Acids; Amino acids;
Adh4 alcohol dehydrogenase 4 121247379 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Steroid Metabolism: Cholesterol Synthesis; Anaplerotic Reactions; Zoosterols; Amino Acids; Amino acids;
Adh5 alcohol dehydrogenase class-3 568384738 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Steroid Metabolism: Cholesterol Synthesis; Anaplerotic Reactions; Zoosterols; Amino Acids; Amino acids;
Adh6 alcohol dehydrogenase 6 254763246 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Steroid Metabolism: Cholesterol Synthesis; Anaplerotic Reactions; Zoosterols; Amino Acids; Amino acids;
Adh7 alcohol dehydrogenase class 4 mu/sigma chain 568921631 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Steroid Metabolism: Cholesterol Synthesis; Anaplerotic Reactions; Zoosterols; Amino Acids; Amino acids;
Adhfe1 hydroxyacid-oxoacid transhydrogenase, mitochondrial * 1039730246
Adk adenosine kinase 19527306 Nucleotide Metabolism: Purines;
Adsl adenylosuccinate lyase 29788764 Nucleotide Metabolism: Purines; Purine Biosynthesis; Purines and Pyrimidines; Purines; Purine Metabolism;
Adss adenylosuccinate synthetase isozyme 2 31560737 Nucleotide Metabolism: Purines; Purines and Pyrimidines; Purines;
Adssl1 adenylosuccinate synthetase isozyme 1 isoform X2 6671519 Nucleotide Metabolism: Purines; Purines and Pyrimidines; Purines;
Afg3l1 AFG3-like protein 1 * 755526291
Afg3l2 AFG3-like protein 2 * 755561255
Afmid kynurenine formamidase 755539745 Amino Acids; Aromatic amino acids;
Agk acylglycerol kinase, mitochondrial 1039775720 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Agmat agmatinase, mitochondrial * 568932038
Agpat1 1-acyl-sn-glycerol-3-phosphate acyltransferase alpha 569001057 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Agpat2 1-acyl-sn-glycerol-3-phosphate acyltransferase beta precursor 1039761748 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Agpat3 1-acyl-sn-glycerol-3-phosphate acyltransferase gamma 568967720 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Agpat4 1-acyl-sn-glycerol-3-phosphate acyltransferase delta 27229064 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Agpat5 1-acyl-sn-glycerol-3-phosphate acyltransferase epsilon 27229077 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Agpat6 glycerol-3-phosphate acyltransferase 6 68052729 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Agpat9 glycerol-3-phosphate acyltransferase 3 1039771324 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Agxt serine--pyruvate aminotransferase, peroxisomal isoform 3 452881620 Citrate and Glyoxalate Cycle; Lipid Metabolism: Glyco- and Phospholipids; Glyoxylate Cycle; Amino Acids; Carbohydrates; Amino acids; TCA Cycle in the Mitochondrial Matrix;
Agxt2 alanine--glyoxylate aminotransferase 2, mitochondrial 568990462 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Citrate and Glyoxalate Cycle; Lipid Metabolism: Glyco- and Phospholipids; Asparate Group of Amino Acids; Branched Chain Amino Acids; Glyoxylate Cycle; Amino Acids; Carbohydrates; Amino acids; TCA Cycle in the Mitochondrial Matrix; Pyrimidine Metabolism;
Ahcy adenosylhomocysteinase 262263372 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids;
Ahcyl1 putative adenosylhomocysteinase 2 27734986 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids;
Ahcyl2 putative adenosylhomocysteinase 3 755515511 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids;
Aicda activation-induced cytidine deaminase 6753018 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Aifm1 apoptosis-inducing factor 1, mitochondrial * 594150372
Aifm2 apoptosis-inducing factor 2 * 755535131
Aifm3 apoptosis-inducing factor 3 * 1039751808
Ak1 adenylate kinase isoenzyme 1 1039758828 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Ak2 adenylate kinase 2, mitochondrial isoform a 77020262 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Ak3 GTP:AMP phosphotransferase AK3, mitochondrial 23956104 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Ak4 adenylate kinase 4, mitochondrial 294862286 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Ak5 adenylate kinase isoenzyme 5 isoform X7 755503815 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Ak6 adenylate kinase isoenzyme 6 28076975 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Ak7 putative adenylate kinase 7 568980728 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Ak8 adenylate kinase 8 152963553 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Ak9 adenylate kinase 9 isoform X7 568966007 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Akd1 adenylate kinase 9 302393675 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Akd2 adenylate kinase 9-like isoform X3 302393675 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Akp1 alkaline phosphatase 1 Lipid Metabolism: Glyco- and Phospholipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines;
Akp3 intestinal-type alkaline phosphatase 2 precursor 110347479 Lipid Metabolism: Glyco- and Phospholipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines;
Akp4 alkaline phosphatase 4 Lipid Metabolism: Glyco- and Phospholipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines;
Akr1a1 alcohol dehydrogenase [NADP(+)] 10946870 Amino Acid Metabolism: Histidine; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pentoses and Pentose Cycle; Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Estrogens; Glucocorticoids; Histidine Metabolism; Mineralcorticoids; Pentose Interconversions; Zoosterols; Amino Acids; Carbohydrates; Amino acids; Glycolysis in the Cytoplasm; Phospholipids; Products of Isoprene Metabolism;
Akr1b1 aldose reductase 113596 Amino Acid Metabolism: Histidine; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pentoses and Pentose Cycle; Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Estrogens; Glucocorticoids; Histidine Metabolism; Mineralcorticoids; Pentose Interconversions; Zoosterols; Amino Acids; Carbohydrates; Amino acids; Glycolysis in the Cytoplasm; Phospholipids; Products of Isoprene Metabolism;
Akr1b10 aldo-keto reductase family 1 member B10 568942706 Amino Acid Metabolism: Histidine; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pentoses and Pentose Cycle; Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Estrogens; Glucocorticoids; Histidine Metabolism; Mineralcorticoids; Pentose Interconversions; Zoosterols; Amino Acids; Carbohydrates; Amino acids; Glycolysis in the Cytoplasm; Phospholipids; Products of Isoprene Metabolism;
Akr1b3 aldose reductase 160707894 Amino Acid Metabolism: Histidine; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pentoses and Pentose Cycle; Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Estrogens; Glucocorticoids; Histidine Metabolism; Mineralcorticoids; Pentose Interconversions; Zoosterols; Amino Acids; Carbohydrates; Amino acids; Glycolysis in the Cytoplasm; Phospholipids; Products of Isoprene Metabolism;
Akr1b7 aldose reductase-related protein 1 160415215 Amino Acid Metabolism: Histidine; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pentoses and Pentose Cycle; Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Estrogens; Glucocorticoids; Histidine Metabolism; Mineralcorticoids; Pentose Interconversions; Zoosterols; Amino Acids; Carbohydrates; Amino acids; Glycolysis in the Cytoplasm; Phospholipids; Products of Isoprene Metabolism;
Akr1b8 aldose reductase-related protein 2 6679791 Amino Acid Metabolism: Histidine; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pentoses and Pentose Cycle; Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Estrogens; Glucocorticoids; Histidine Metabolism; Mineralcorticoids; Pentose Interconversions; Zoosterols; Amino Acids; Carbohydrates; Amino acids; Glycolysis in the Cytoplasm; Phospholipids; Products of Isoprene Metabolism;
Akr1c1 aldo-keto reductase family 1, member C1 416877 Amino Acid Metabolism: Histidine; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pentoses and Pentose Cycle; Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Estrogens; Glucocorticoids; Histidine Metabolism; Mineralcorticoids; Pentose Interconversions; Zoosterols; Amino Acids; Carbohydrates; Amino acids; Glycolysis in the Cytoplasm; Phospholipids; Products of Isoprene Metabolism;
Akr1c2 aldo-keto reductase family 1 member C21 20532374 Amino Acid Metabolism: Histidine; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pentoses and Pentose Cycle; Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Estrogens; Glucocorticoids; Histidine Metabolism; Mineralcorticoids; Pentose Interconversions; Zoosterols; Amino Acids; Carbohydrates; Amino acids; Glycolysis in the Cytoplasm; Phospholipids; Products of Isoprene Metabolism;
Akr1c3 aldo-keto reductase family 1 member C18 308153646 Amino Acid Metabolism: Histidine; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pentoses and Pentose Cycle; Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Estrogens; Glucocorticoids; Histidine Metabolism; Mineralcorticoids; Pentose Interconversions; Zoosterols; Amino Acids; Carbohydrates; Amino acids; Glycolysis in the Cytoplasm; Phospholipids; Products of Isoprene Metabolism;
Akr1d1 3-oxo-5-beta-steroid 4-dehydrogenase 21703734 Amino Acid Metabolism: Histidine; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pentoses and Pentose Cycle; Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Estrogens; Glucocorticoids; Histidine Metabolism; Mineralcorticoids; Pentose Interconversions; Zoosterols; Amino Acids; Carbohydrates; Amino acids; Glycolysis in the Cytoplasm; Phospholipids; Products of Isoprene Metabolism;
Akr1e2 1,5-anhydro-D-fructose reductase 269849539 Amino Acid Metabolism: Histidine; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pentoses and Pentose Cycle; Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Estrogens; Glucocorticoids; Histidine Metabolism; Mineralcorticoids; Pentose Interconversions; Zoosterols; Amino Acids; Carbohydrates; Amino acids; Glycolysis in the Cytoplasm; Phospholipids; Products of Isoprene Metabolism;
Akr7a5 aflatoxin B1 aldehyde reductase member 2* 240120054
Alad delta-aminolevulinic acid dehydratase 568926120 Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Porphyrins; Vitamins, Co-Enzymes, and Hormones; Porphyrins; Heme Metabolism;
Alas1 5-aminolevulinate synthase, nonspecific, mitochondrial precursor 628601867 Citrate and Glyoxalate Cycle; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Glyoxylate Cycle; Porphyrins; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Heme Metabolism;
Alas2 5-aminolevulinate synthase, erythroid-specific, mitochondrial 156255176 Citrate and Glyoxalate Cycle; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Glyoxylate Cycle; Porphyrins; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Heme Metabolism;
Aldh18a1 delta-1-pyrroline-5-carboxylate synthase 255958294 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh1a1 retinal dehydrogenase 1 85861182 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh1a2 retinal dehydrogenase 2 225735569 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh1a3 aldehyde dehydrogenase family 1 member A3 170650621 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh1a7 aldehyde dehydrogenase, cytosolic 1 7106242 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh1b1 aldehyde dehydrogenase X, mitochondrial precursor 21312260 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh1l1 cytosolic 10-formyltetrahydrofolate dehydrogenase 568940123 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh1l2 10-formyltetrahydrofolate dehydrogenase ALDH1L2 755534371 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh2 aldehyde dehydrogenase, mitochondrial precursor 817379474 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh3a1 aldehyde dehydrogenase, dimeric NADP-preferring 1062593982 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh3a2 fatty aldehyde dehydrogenase 1062594028 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh3b1 aldehyde dehydrogenase family 3 member B1 569005967 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh3b2 aldehyde dehydrogenase family 3 member B1 294460012 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh4a1 delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial 568930882 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh5a1 succinate-semialdehyde dehydrogenase, mitochondrial precursor 27369748 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh6a1 methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial precursor 1039739590 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh7a1 alpha-aminoadipic semialdehyde dehydrogenase 188219757 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldh9a1 4-trimethylaminobutyraldehyde dehydrogenase 115334671 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Lysine; Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrate Metabolism: Pyruvate Turnover; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Glyco- and Phospholipids; Steroid Metabolism: Cholesterol Synthesis; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Anaplerotic Reactions; Carotenoids; Glutamate Decarboxylation Pathway; Histidine Metabolism; Lysine Metabolism; Mesaconate Pathway; Porphyrins; Zoosterols; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism; Pyrimidine Metabolism;
Aldoa fructose-bisphosphate aldolase A 568949352 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Glycolysis and TCA Cycle; Pentose Phosphate Pathways;
Aldoart1 aldolase 1 A retrogene 1 312922382 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Glycolysis and TCA Cycle; Pentose Phosphate Pathways;
Aldoart2 fructose-bisphosphate aldolase 476007882 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Glycolysis and TCA Cycle; Pentose Phosphate Pathways;
Aldob fructose-bisphosphate aldolase B 21450291 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Glycolysis and TCA Cycle; Pentose Phosphate Pathways;
Aldoc fructose-bisphosphate aldolase C 742670581 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Carbohydrates; Vitamins, Co-Enzymes, and Hormones; Glycolysis in the Cytoplasm; Isoprenoids; Glycolysis and TCA Cycle; Isoprene Metabolism; Pentose Phosphate Pathways; Products of Isoprene Metabolism;
Allc allantoicase 568978162 Nucleotide Metabolism: Purines; Purines; Purines and Pyrimidines; Purines; Purine Metabolism;
Alox15 arachidonate 15-lipoxygenase 568971264 Prostaglandins, Thromboxanes, and Leucotrienes;
Alox15b arachidonate 15-lipoxygenase B 317373425 Prostaglandins, Thromboxanes, and Leucotrienes;
Alox5 arachidonate 5-lipoxygenase 62526037 Lipids; Lipid biosynthesis;
Alpi intestinal-type alkaline phosphatase 1 precursor 124487323 Lipid Metabolism: Glyco- and Phospholipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines;
Alpl alkaline phosphatase, tissue-nonspecific isozyme precursor 563317855 Lipid Metabolism: Glyco- and Phospholipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines;
Alpp alkaline phosphatase, placental-like 130737 Lipid Metabolism: Glyco- and Phospholipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines;
Alppl2 alkaline phosphatase, placental-like 755493723 Lipid Metabolism: Glyco- and Phospholipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines;
Amacr alpha-methylacyl-CoA racemase* 46518506
Amdhd1 imidazolonepropionase 568968650 Amino Acid Metabolism: Histidine; Histidine Metabolism; Amino Acids; Amino acids;
Amdhd2 putative N-acetylglucosamine-6-phosphate deacetylase 31982133 Amino Acid Metabolism: Histidine; Histidine Metabolism; Amino Acids; Amino acids;
Ampd1 AMP deaminase 1 568922626 Nucleotide Metabolism: Purines; Purine Metabolism;
Ampd2 AMP deaminase 2 1039763603 Nucleotide Metabolism: Purines; Purine Metabolism;
Ampd3 AMP deaminase 3 1039776976 Nucleotide Metabolism: Purines; Purine Metabolism;
Amt aminomethyltransferase, mitochondrial 755531362 C1-Metabolism; One Carbon Pool; Folic Acid Metabolism; Folic Acid Reactions;
Amy1 alpha-amylase 1 precursor 160358821 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Amy1a alpha-amylase 1 precursor 1351933 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Amy1b alpha-amylase 1 precursor 1351933 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Amy1c alpha-amylase 1 precursor 1351933 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Amy2-3 pancreatic alpha-amylase 21542378 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Amy2a pancreatic alpha-amylase precursor 4502085 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Amy2a1 pancreatic alpha-amylase 755505873 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Amy2a2 amylase 2a2 precursor 236468330 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Amy2a3 pancreatic alpha-amylase precursor 236468206 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Amy2a4 amylase 2a4 precursor 236468117 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Amy2a5 pancreatic alpha-amylase precursor 111607467 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Amy2b amylase 2b isoform 2 precursor 298676470 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Aoc1 amiloride-sensitive amine oxidase [copper-containing] precursor 239051904 Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Urea Cycle; Histidine Metabolism; Urea Cycle;
Aoc2 retina-specific copper amine oxidase 1039737127 Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Urea Cycle; Histidine Metabolism; Urea Cycle;
Aoc2-ps1 amine oxidase, copper containing 2 (retina-specific), pseudogene 1 Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Urea Cycle; Histidine Metabolism; Urea Cycle;
Aoc3 membrane primary amine oxidase 1039735447 Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Urea Cycle; Histidine Metabolism; Urea Cycle;
Aox1 aldehyde oxidase 1 568905650 Amino Acid Metabolism: Histidine; Histidine Metabolism;
Aox2 aldehyde oxidase 2 1039728228 Amino Acid Metabolism: Histidine; Histidine Metabolism;
Aox3 aldehyde oxidase 3 114205420 Amino Acid Metabolism: Histidine; Histidine Metabolism;
Aox4 aldehyde oxidase 4 568906985 Amino Acid Metabolism: Histidine; Histidine Metabolism;
Apoa1bp NAD(P)H-hydrate epimerase * 21553309
Apobec1 C->U-editing enzyme APOBEC-1 755515931 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Apobec2 C->U-editing enzyme APOBEC-2 6753098 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Apobec3 DNA dC->dU-editing enzyme APOBEC-3 isoform 1 1039749741 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Apobec4 putative C->U-editing enzyme APOBEC-4 124487115 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Aprt adenine phosphoribosyltransferase 118601013 Nucleotide Metabolism: Purines; Purine Metabolism;
Arg1 arginase-1 7106255 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids;
Arg2 arginase-2, mitochondrial precursor 6753110 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids;
Arsa arylsulfatase A precursor 67972647 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Citrate and Glyoxalate Cycle; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Estrogens; Glyoxylate Cycle; Porphyrins; Sulfur Metabolism; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Heme Metabolism;
Arsb arylsulfatase B precursor 125656171 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Citrate and Glyoxalate Cycle; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Estrogens; Glyoxylate Cycle; Porphyrins; Sulfur Metabolism; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Heme Metabolism;
Arsd arylsulfatase D precursor 71852584 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Citrate and Glyoxalate Cycle; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Estrogens; Glyoxylate Cycle; Porphyrins; Sulfur Metabolism; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Heme Metabolism;
Arse arylsulfatase E precursor 114145540 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Citrate and Glyoxalate Cycle; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Estrogens; Glyoxylate Cycle; Porphyrins; Sulfur Metabolism; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Heme Metabolism;
Arsf arylsulfatase F precursor 31742482 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Citrate and Glyoxalate Cycle; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Estrogens; Glyoxylate Cycle; Porphyrins; Sulfur Metabolism; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Heme Metabolism;
Arsg arylsulfatase G precursor 1039738458 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Citrate and Glyoxalate Cycle; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Estrogens; Glyoxylate Cycle; Porphyrins; Sulfur Metabolism; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Heme Metabolism;
Arsh arylsulfatase H 58743319 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Citrate and Glyoxalate Cycle; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Estrogens; Glyoxylate Cycle; Porphyrins; Sulfur Metabolism; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Heme Metabolism;
Arsi arylsulfatase I precursor 755561108 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Citrate and Glyoxalate Cycle; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Estrogens; Glyoxylate Cycle; Porphyrins; Sulfur Metabolism; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Heme Metabolism;
Arsj arylsulfatase J 27734088 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Citrate and Glyoxalate Cycle; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Estrogens; Glyoxylate Cycle; Porphyrins; Sulfur Metabolism; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Heme Metabolism;
Arsk arylsulfatase K precursor 148277048 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Citrate and Glyoxalate Cycle; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Estrogens; Glyoxylate Cycle; Porphyrins; Sulfur Metabolism; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Heme Metabolism;
As3mt arsenite methyltransferase * 755563485
Asah1 acid ceramidase precursor 1039781560 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Asah2 neutral ceramidase 755563427 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Asah2c putative neutral ceramidase C 206557840 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Asl argininosuccinate lyase 1039770204 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids; Deamination of Amino Acids: The Urea Cycle;
Asmt acetylserotonin O-methyltransferase 819231728 Vitamins, Co-Enzymes, and Hormones; Aromatic amino acids;
Asns asparagine synthetase [glutamine-hydrolyzing] 568939636 Amino Acids; Amino acids;
Aspg 60 kDa lysophospholipase 568978556 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Asparate Group of Amino Acids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids;
Asrgl1 isoaspartyl peptidase/L-asparaginase 31560239 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Asparate Group of Amino Acids;
Ass1 argininosuccinate synthase 6996911 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids; Deamination of Amino Acids: The Urea Cycle;
Atad1 ATPase family AAA domain-containing protein 1 569007752 Nucleotide Metabolism: Purines;
Atad2 ATPase family AAA domain-containing protein 2 91199557 Nucleotide Metabolism: Purines;
Atad3a ATPase family AAA domain-containing protein 3 568930415 Nucleotide Metabolism: Purines;
Atad3b ATPase family AAA domain-containing protein 3B 13994294 Nucleotide Metabolism: Purines;
Atad3c ATPase family AAA domain-containing protein 3C 194018490 Nucleotide Metabolism: Purines;
Atic phosphoribosylaminoimidazolecarboxamide formyltransferase 227908823 C1-Metabolism; Nucleotide Metabolism: Purines; One Carbon Pool; Purine Biosynthesis; Purines and Pyrimidines; Purines; Folic Acid Metabolism; Folic Acid Reactions; Purine Metabolism;
Atp10a phospholipid-transporting ATPase VA 157951686 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp1a1 sodium/potassium-transporting ATPase subunit alpha-1 precursor 21450277 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp1a2 sodium/potassium-transporting ATPase subunit alpha-2 precursor 30409956 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp1a3 sodium/potassium-transporting ATPase subunit alpha-3 755519440 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp1a4 sodium/potassium-transporting ATPase subunit alpha-4 568910919 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp1b1 sodium/potassium-transporting ATPase subunit beta-1 6753138 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp1b2 sodium/potassium-transporting ATPase subunit beta-2 1039735454 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp1b3 sodium/potassium-transporting ATPase subunit beta-3 1039791993 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp1b4 X,K-ATPase subunit beta-m 569009373 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp2b1 plasma membrane calcium-transporting ATPase 1 1039734048 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp2b2 plasma membrane calcium-transporting ATPase 2 80861454 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp2b3 plasma membrane calcium-transporting ATPase 3 755565498 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp2b4 plasma membrane calcium-transporting ATPase 4 755494464 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp4b potassium-transporting ATPase subunit beta 6753142 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5a1 ATP synthase subunit alpha, mitochondrial precursor 6680748 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5b ATP synthase subunit beta, mitochondrial precursor 31980648 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5c1 ATP synthase subunit gamma, mitochondrial 568912066 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5d ATP synthase subunit delta, mitochondrial precursor 1039733922 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5e ATP synthase subunit epsilon, mitochondrial 13385484 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5f1 ATP synthase F(0) complex subunit B1, mitochondrial precursor 754170607 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5g1 ATP synthase F(0) complex subunit C1, mitochondrial precursor 238637299 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5g2 ATP synthase F(0) complex subunit C2, mitochondrial precursor 13385960 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5g3 ATP synthase F(0) complex subunit C3, mitochondrial precursor 683523931 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5h ATP synthase subunit d, mitochondrial 21313679 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5i ATP synthase subunit e, mitochondrial 17978459 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5j ATP synthase-coupling factor 6, mitochondrial precursor 7949005 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5j2 ATP synthase subunit f, mitochondrial 10181184 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5l ATP synthase subunit g, mitochondrial 31980744 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp5o ATP synthase subunit O, mitochondrial * 20070412
Atp6v0a1 V-type proton ATPase 116 kDa subunit a isoform 1 568971302 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v0a2 V-type proton ATPase 116 kDa subunit a isoform 2 83627707 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v0a4 V-type proton ATPase 116 kDa subunit a isoform 4 171543866 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v0b V-type proton ATPase 21 kDa proteolipid subunit 15991795 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v0c V-type proton ATPase 16 kDa proteolipid subunit 6753144 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v0d1 V-type proton ATPase subunit d 1 31981304 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v0d2 V-type proton ATPase subunit d 2 1039767634 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v0e1 V-type proton ATPase subunit e 1 50659077 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v1a V-type proton ATPase catalytic subunit A 31560731 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v1b1 V-type proton ATPase subunit B, kidney isoform 19527064 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v1b2 V-type proton ATPase subunit B, brain isoform 19705578 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v1c1 V-type proton ATPase subunit C 1 189339262 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v1c2 V-type proton ATPase subunit C 2 1039741831 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v1d V-type proton ATPase subunit D 12963799 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v1e1 V-type proton ATPase subunit E 1 45504359 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v1e2 V-type proton ATPase subunit E 2 254911018 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v1f V-type proton ATPase subunit F 21314824 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v1g1 V-type proton ATPase subunit G 1 15617197 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v1g2 V-type proton ATPase subunit G 2 569001361 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v1g3 V-type proton ATPase subunit G 3 28893577 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp6v1h V-type proton ATPase subunit H 1039727271 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Atp8a1 phospholipid-transporting ATPase IA isoform X8 1039770334 Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Auh methylglutaconyl-CoA hydratase, mitochondrial isoform X2 1039743073 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids; Amino Acids; Carbohydrates; Amino acids; ATP Formation Spanning the Mitochondrial Inner Membrane;
Awat1 acyl-CoA wax alcohol acyltransferase 1 124487273 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Awat2 acyl-CoA wax alcohol acyltransferase 2 1039797330 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
B3galt1 beta-1,3-galactosyltransferase 1 1039760781 Lipids; Phospholipids;
B3galt2 beta-1,3-galactosyltransferase 2 157266277 Lipids; Phospholipids;
B3galt4 beta-1,3-galactosyltransferase 4 9506417 Lipids; Phospholipids;
B3galt5 beta-1,3-galactosyltransferase 5 isoform X1 1039752003 Lipids; Phospholipids;
B3galt6 beta-1,3-galactosyltransferase 6 17978260 Lipids; Phospholipids;
B4galt1 beta-1,4-galactosyltransferase 1 568926081 Carbohydrate Metabolism: Di-and Polysaccharides; Carbohydrates; Polysaccharides;
B4galt2 beta-1,4-galactosyltransferase 2 358356400 Carbohydrate Metabolism: Di-and Polysaccharides; Carbohydrates; Polysaccharides;
B4galt3 beta-1,4-galactosyltransferase 3 224809362 Carbohydrate Metabolism: Di-and Polysaccharides; Carbohydrates; Polysaccharides;
B4galt4 beta-1,4-galactosyltransferase 4 755553849 Carbohydrate Metabolism: Di-and Polysaccharides; Carbohydrates; Polysaccharides;
B4galt5 beta-1,4-galactosyltransferase 5 116089306 Carbohydrate Metabolism: Di-and Polysaccharides; Carbohydrates; Polysaccharides;
B4galt6 beta-1,4-galactosyltransferase 6 9790037 Carbohydrate Metabolism: Di-and Polysaccharides; Carbohydrates; Polysaccharides;
B4galt7 beta-1,4-galactosyltransferase 7 902763324 Carbohydrate Metabolism: Di-and Polysaccharides; Carbohydrates; Polysaccharides;
Baat bile acid-CoA:amino acid N-acyltransferase 568925970 Steroid Metabolism: Cholesterol Synthesis; Bile Acids;
Bbox1 gamma-butyrobetaine dioxygenase 568915590 Amino Acids; Amino acids;
Bbox2 trimethyllysine dioxygenase, mitochondrial 20270297 Amino Acids; Amino acids;
Bcat1 branched-chain-amino-acid aminotransferase, cytosolic 66792792 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids; Deamination of Amino Acids: The Urea Cycle;
Bcat2 branched-chain-amino-acid aminotransferase, mitochondrial precursor 1039777058 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids; Deamination of Amino Acids: The Urea Cycle;
Bckdha 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial 568944746 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids;
Bckdhb 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial precursor 1039791995 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids;
Bckdk [3-methyl-2-oxobutanoate dehydrogenase [lipoamide]] kinase, mitochondrial precursor 6753164 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids;
Bcmo1 beta,beta-carotene 15,15'-monooxygenase isoform 2 253314530 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Bdh1 D-beta-hydroxybutyrate dehydrogenase, mitochondrial 170014725 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipid biosynthesis;
Bdh2 3-hydroxybutyrate dehydrogenase type 2 285026426 Lipid Metabolism: Fatty Acids; Ketone Bodies; Lipid biosynthesis;
Bhmt betaine--homocysteine S-methyltransferase 1 7709990 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Lipid Metabolism: Glyco- and Phospholipids; Sulfur Metabolism; Amino Acids; Amino acids;
Bhmt2 S-methylmethionine--homocysteine S-methyltransferase BHMT2 145553963 Amino Acids; Amino acids;
Blvra biliverdin reductase A precursor 568915059 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
Blvrb flavin reductase 594542552 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
Bp3 ADP-ribosyl cyclase/cyclic ADP-ribose hydrolase 2 precursor 134288869 Nucleotide Metabolism: NAD, NADP;
Bpgm bisphosphoglycerate mutase 568940405 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis;
Bphl valacyclovir hydrolase * 568981956
Bpnt1 3'(2'),5'-bisphosphate nucleotidase 1 39652626 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Bst1 ADP-ribosyl cyclase/cyclic ADP-ribose hydrolase 2 precursor 568933707 Nucleotide Metabolism: NAD, NADP;
C12orf5 fructose-2,6-bisphosphatase TIGAR 9966849 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis;
Cad caspase-activated deoxyribonuclease 568934508 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Amino Acids; Purines and Pyrimidines; Amino acids; Pyrimidines; Pyrimidine Metabolism;
Cant1 soluble calcium-activated nucleotidase 1 390125187 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Car5a carbonic anhydrase 5A, mitochondrial * 112181175
Car5b carbonic anhydrase 5B, mitochondrial * 211057396
Carns1 carnosine synthase 1-like isoform X3 1039757032 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Asparate Group of Amino Acids;
Cars2 probable cysteine--tRNA ligase, mitochondrial * 189409152
Casp1 caspase-1* 86198305
Casp12 caspase-12* 157951684
Casp2 caspase-2 * 568940489
Casp3 caspase-3* 549806822
Casp4 caspase-4 * 568958482
Casp6 caspase-6 * 157951736
Casp7 caspase-7 * 569006271
Casp8 caspase-8 * 568905658
Casp9 caspase-9 * 485050375
Cat catalase* 157951741
Cbr1 carbonyl reductase [NADPH] 1* 113680352
Cbr2 carbonyl reductase [NADPH] 2 * 568971391
Cbr3 carbonyl reductase [NADPH] 3* 27413160
Cbr4 carbonyl reductase family member 4* 269784762
Cbs cystathionine beta-synthase 568998791 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids;
Ccbl1 kynurenine--oxoglutarate transaminase 1, mitochondrial 148356231 Nucleotide Metabolism: NAD, NADP;
Ccbl2 kynurenine--oxoglutarate transaminase 3 62543563 Citrate and Glyoxalate Cycle; Lipid Metabolism: Glyco- and Phospholipids; Nucleotide Metabolism: NAD, NADP; Glyoxylate Cycle; Amino Acids; Carbohydrates; Amino acids; TCA Cycle in the Mitochondrial Matrix;
Cd38 ADP-ribosyl cyclase/cyclic ADP-ribose hydrolase 1 31542362 Nucleotide Metabolism: NAD, NADP;
Cda cytidine deaminase 568931934 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Cdipt CDP-diacylglycerol--inositol 3-phosphatidyltransferase 1039779244 Carbohydrate Metabolism: Inositol; Lipid Metabolism: Glyco- and Phospholipids; Inositol Metabolism; Lipids; Phospholipids;
Cdo1 cysteine dioxygenase type 1 14719434 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids;
Cds1 phosphatidate cytidylyltransferase 1 568936303 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Phospholipids;
Cds2 phosphatidate cytidylyltransferase 2 755498549 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Phospholipids;
Cel bile salt-activated lipase precursor 6753406 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Carotenoids; Fatty Acid Oxidation; Zoosterols; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Cept1 choline/ethanolaminephosphotransferase 1 1039765595 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Phospholipids;
Cers1 ceramide synthase 1 20149718 Lipid Metabolism: Sphingolipids;
Cers2 LAG1 homolog, ceramide synthase 2 568924431 Lipid Metabolism: Sphingolipids;
Cers3 ceramide synthase 3 755521153 Lipid Metabolism: Sphingolipids;
Cers4 ceramide synthase 4 568953457 Lipid Metabolism: Sphingolipids;
Cers5 ceramide synthase 5 21312638 Lipid Metabolism: Sphingolipids;
Cers6 ceramide synthase 6 isoform X1 1039760565 Lipid Metabolism: Sphingolipids;
Ces1a carboxylesterase 1-like precursor 1039789971 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Products of Isoprene Metabolism;
Ces1b carboxylesterase 1B precursor 568957113 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Products of Isoprene Metabolism;
Ces1c carboxylesterase 1C precursor 247269929 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Products of Isoprene Metabolism;
Ces1d carboxylesterase 1D precursor 117553604 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Products of Isoprene Metabolism;
Ces1e carboxylesterase 1E precursor 19526804 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Products of Isoprene Metabolism;
Ces1f liver carboxylesterase 4 precursor 21450339 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Products of Isoprene Metabolism;
Ces1g liver carboxylesterase 1 precursor 162287349 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Products of Isoprene Metabolism;
Ces1h carboxylesterase 1E isoform X2 1039791441 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Products of Isoprene Metabolism;
Ces2 carboxylesterase 2 precursor 404351669 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Carotenoids; Ketone Bodies; Zoosterols; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid degradation; Lipid Metabolism; Products of Isoprene Metabolism;
Ces2a pyrethroid hydrolase Ces2a 298358786 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Carotenoids; Ketone Bodies; Zoosterols; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid degradation; Lipid Metabolism; Products of Isoprene Metabolism;
Ces2b carboxyesterase 2B precursor 568956567 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Carotenoids; Ketone Bodies; Zoosterols; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid degradation; Lipid Metabolism; Products of Isoprene Metabolism;
Ces2c carboxylesterase 2C precursor 21704206 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Carotenoids; Ketone Bodies; Zoosterols; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid degradation; Lipid Metabolism; Products of Isoprene Metabolism;
Ces2e carboxylesterase 5 precursor 254939648 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Carotenoids; Ketone Bodies; Zoosterols; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid degradation; Lipid Metabolism; Products of Isoprene Metabolism;
Ces2f carboxylesterase 2F precursor 568957601 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Carotenoids; Ketone Bodies; Zoosterols; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid degradation; Lipid Metabolism; Products of Isoprene Metabolism;
Ces2g carboxylesterase 2G precursor 568957621 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Carotenoids; Ketone Bodies; Zoosterols; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid degradation; Lipid Metabolism; Products of Isoprene Metabolism;
Ces2h carboxylesterase 2 isoform 2 precursor 440309855 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Carotenoids; Ketone Bodies; Zoosterols; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid degradation; Lipid Metabolism; Products of Isoprene Metabolism;
Ces2i pyrethroid hydrolase Ces2a-like isoform X5 564334564 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Carotenoids; Ketone Bodies; Zoosterols; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid degradation; Lipid Metabolism; Products of Isoprene Metabolism;
Ces2j carboxylesterase 2J precursor 334358886 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Carotenoids; Ketone Bodies; Zoosterols; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid degradation; Lipid Metabolism; Products of Isoprene Metabolism;
Ces3 carboxylesterase 3 isoform 2 precursor 297747275 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Products of Isoprene Metabolism;
Ces3a carboxylesterase 3B-like 257743054 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Products of Isoprene Metabolism;
Ces3b carboxylesterase 3B isoform 2 precursor 1039782586 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Products of Isoprene Metabolism;
Ces5a carboxylesterase 5A precursor 568957473 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Products of Isoprene Metabolism;
Cesl1 liver carboxylesterase B-1 precursor 66730527 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Products of Isoprene Metabolism;
Chat choline O-acetyltransferase 45476575 Lipid Metabolism: Glyco- and Phospholipids; Lipids; Phospholipids;
Chdh choline dehydrogenase, mitochondrial 210031293 Lipid Metabolism: Glyco- and Phospholipids; Amino Acids; Amino acids;
Chka choline kinase alpha 1039757117 Lipid Metabolism: Glyco- and Phospholipids; Lipids; Phospholipids;
Chkb choline/ethanolamine kinase 6671748 Lipid Metabolism: Glyco- and Phospholipids; Lipids; Phospholipids;
Chpt1 cholinephosphotransferase 1 568967159 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Lipids; Phospholipids;
Chst1 carbohydrate sulfotransferase 1 precursor 568918843 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst10 carbohydrate sulfotransferase 10 precursor 568907151 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst11 carbohydrate sulfotransferase 11 568968106 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst12 carbohydrate sulfotransferase 12 isoform X3 568938765 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst13 carbohydrate sulfotransferase 13 precursor 254692861 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst14 carbohydrate sulfotransferase 14 254540084 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst15 carbohydrate sulfotransferase 15 1039780313 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst2 carbohydrate sulfotransferase 2 157266319 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst3 carbohydrate sulfotransferase 3 1039733797 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst4 carbohydrate sulfotransferase 4 isoform X2 568956891 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst5 carbohydrate sulfotransferase 5 9910284 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst6 carbohydrate sulfotransferase 6 precursor 11055976 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst7 carbohydrate sulfotransferase 7 precursor 11096336 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst8 carbohydrate sulfotransferase 8 568946521 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Chst9 carbohydrate (N-acetylgalactosamine 4-0) sulfotransferase 9 1039756481 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Mesaconate Pathway; Sulfur Metabolism;
Ckb creatine kinase B-type 10946574 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids;
Ckm creatine kinase M-type 6671762 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids;
Ckmt1 creatine kinase U-type, mitochondrial precursor 568915235 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids;
Ckmt1a creatine kinase U-type, mitochondrial precursor 66346730 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids;
Ckmt1b creatine kinase U-type, mitochondrial precursor 60678254 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids;
Ckmt2 creatine kinase S-type, mitochondrial precursor 568983791 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids;
Clybl citrate lyase subunit beta-like protein, mitochondrial * 256220113
Cmas N-acylneuraminate cytidylyltransferase 247269309 Carbohydrate Metabolism: Amino Sugar Derivatives; Amino Sugars; Carbohydrates; Polysaccharides;
Cmpk1 UMP-CMP kinase 165377065 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Cmpk2 UMP-CMP kinase 2, mitochondrial 117606366 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Coasy bifunctional coenzyme A synthase precursor 1039738290 Cofactors and Vitamins: Coenzyme A; Vitamins, Co-Enzymes, and Hormones; Amino acids;
Colgalt1 procollagen galactosyltransferase 1 precursor 755525928 Amino Acid Metabolism: Lysine; Lysine Metabolism;
Colgalt2 procollagen galactosyltransferase 2 228008340 Amino Acid Metabolism: Lysine; Lysine Metabolism;
Comt catechol O-methyltransferase 161484638 Vitamins, Co-Enzymes, and Hormones; Catecholamines;
Comtd1 catechol O-methyltransferase domain-containing protein 1* 33468999
Coq2 4-hydroxybenzoate polyprenyltransferase, mitochondrial * 167004227
Coq3 ubiquinone biosynthesis O-methyltransferase, mitochondrial* 27369992
Coq4 ubiquinone biosynthesis protein COQ4 homolog, mitochondrial * 1039760066
Coq5 2-methoxy-6-polyprenyl-1,4-benzoquinol methylase, mitochondrial * 13385992
Coq6 ubiquinone biosynthesis monooxygenase COQ6, mitochondrial * 568979303
Coq7 5-demethoxyubiquinone hydroxylase, mitochondrial * 756141038
Coq8a atypical kinase ADCK3, mitochondrial* 254028217
Coq8b aarF domain-containing protein kinase 4* 124244100
Coq9 ubiquinone biosynthesis protein COQ9, mitochondrial * 33859690
Cox1 cytochrome c oxidase subunit I (mitochondrion) 1037241541 Lipids; Lipid biosynthesis;
Cox10 protoheme IX farnesyltransferase, mitochondrial * 568975719
Cox11 cytochrome c oxidase assembly protein COX11, mitochondrial* 39841021
Cox14 cytochrome c oxidase assembly protein COX14* 34304032
Cox15 cytochrome c oxidase assembly protein COX15 homolog* 31541932
Cox16 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial * 831360268
Cox17 cytochrome c oxidase copper chaperone* 62945234
Cox18 mitochondrial inner membrane protein COX18 * 1039771296
Cox19 cytochrome c oxidase assembly protein COX19* 37574050
Cox2 cytochrome c oxidase subunit II (mitochondrion) 1037241542 Lipids; Lipid biosynthesis;
Cox20 cytochrome c oxidase protein 20 homolog* 21313516
Cox3 cytochrome c oxidase subunit III (mitochondrion)* 1037241545
Cox4i1 cytochrome c oxidase subunit 4 isoform 1, mitochondrial precursor 651165917 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox4i2 cytochrome c oxidase subunit 4 isoform 2, mitochondrial isoform 2 precursor 1039762377 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox5a cytochrome c oxidase subunit 5A, mitochondrial precursor 112181182 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox5b cytochrome c oxidase subunit 5B, mitochondrial precursor 112807195 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox6a1 cytochrome c oxidase subunit 6A1, mitochondrial precursor 6680988 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox6a2 cytochrome c oxidase subunit 6A2, mitochondrial precursor 83816956 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox6b1 cytochrome c oxidase subunit 6B1 13385090 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox6b2 cytochrome c oxidase subunit 6B2 577861048 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox6c cytochrome c oxidase subunit 6C-2 16716343 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox6c2 cytochrome c oxidase subunit 6C-2 160333459 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox7a1 cytochrome c oxidase subunit 7A1, mitochondrial * 6753504
Cox7a2 cytochrome c oxidase subunit 7A2, mitochondrial precursor 31981830 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox7a2l cytochrome c oxidase subunit VIIa polypeptide 2 like 226958512 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox7b cytochrome c oxidase subunit 7B, mitochondrial precursor 13384754 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox7b2 cytochrome c oxidase subunit 7B2, mitochondrial isoform X2 27229253 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox7c cytochrome c oxidase subunit 7C, mitochondrial 6680991 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox8a cytochrome c oxidase subunit 8A, mitochondrial precursor 6680993 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox8b cytochrome c oxidase subunit 8B, mitochondrial precursor 6680995 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cox8c cytochrome c oxidase subunit 8C, mitochondrial 84794657 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Cp ceruloplasmin isoform 2 precursor 442745910 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
Cpox oxygen-dependent coproporphyrinogen-III oxidase, mitochondrial precursor 161484660 Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Porphyrins; Vitamins, Co-Enzymes, and Hormones; Porphyrins; Heme Metabolism;
Cps1 carbamoyl-phosphate synthase [ammonia], mitochondrial precursor 755492408 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids; Deamination of Amino Acids: The Urea Cycle;
Cpt1a carnitine O-palmitoyltransferase 1, liver isoform 755562317 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids;
Cpt1b carnitine O-palmitoyltransferase 1, muscle isoform 162287165 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids;
Cpt1c carnitine O-palmitoyltransferase 1, brain isoform 755521384 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids;
Cpt2 carnitine O-palmitoyltransferase 2, mitochondrial precursor 162138915 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids;
Crat carnitine O-acetyltransferase 568912868 Citrate and Glyoxalate Cycle; Citrate Cycle; Lipids; Lipid degradation; Lipid Metabolism;
Crls1 cardiolipin synthase (CMP-forming) * 568918052
Crot peroxisomal carnitine O-octanoyltransferase * 568932855
Cryl1 L-gulonate 3-dehydrogenase 19525729 Carbohydrates; Hexoses;
Cs citrate synthase, mitochondrial precursor 13385942 Citrate and Glyoxalate Cycle; Glyoxylate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle; Lipid Metabolism;
Csad cysteine sulfinic acid decarboxylase isoform 2 1039748921 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids;
Cth cystathionine gamma-lyase 568921412 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids;
Ctps1 CTP synthase 1 199560247 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Pyrimidines; Pyrimidine Metabolism;
Ctps2 CTP synthase 2 569012126 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Pyrimidines; Pyrimidine Metabolism;
Ctu1 cytoplasmic tRNA 2-thiolation protein 1 * 1039778275
Ctu2 cytoplasmic tRNA 2-thiolation protein 2 * 755527181
Cyb5r1 NADH-cytochrome b5 reductase 1 21312524 Vitamins, Co-Enzymes, and Hormones; Hexoses;
Cyb5r2 NADH-cytochrome b5 reductase 2 1039779004 Vitamins, Co-Enzymes, and Hormones; Hexoses;
Cyb5r3 NADH-cytochrome b5 reductase 3 755550818 Vitamins, Co-Enzymes, and Hormones; Hexoses;
Cyb5r4 cytochrome b5 reductase 4 1039793335 Vitamins, Co-Enzymes, and Hormones; Hexoses;
Cyp11a1 cholesterol desmolase 1039792034 Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Corticoids and Gestagens; Zoosterols; Isoprene Metabolism;
Cyp11b1 steroid 11-beta-hydroxylase 269914148 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Glucocorticoids; Mineralcorticoids; Isoprene Metabolism;
Cyp11b2 steroid 11-beta-hydroxylase 226823208 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Glucocorticoids; Mineralcorticoids; Isoprene Metabolism;
Cyp11b3 steroid 11-beta-hydroxylase 32452542 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Glucocorticoids; Mineralcorticoids; Isoprene Metabolism;
Cyp17a1 steroid 17-alpha-hydroxylase/17,20 lyase precursor 160948601 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Corticoids and Gestagens; Gestagen; Zoosterols; Isoprene Metabolism;
Cyp19a1 aromatase 1039792038 Steroid Metabolism: Androgens and Estrogens; Androgens; Estrogens;
Cyp21 steroid 21-hydroxylase 259906405 Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Corticoids and Gestagens; Gestagen; Glucocorticoids; Isoprene Metabolism;
Cyp21a1 steroid 21-hydroxylase 160948604 Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Corticoids and Gestagens; Gestagen; Glucocorticoids; Isoprene Metabolism;
Cyp21a2 steroid 21-hydroxylase isoform b 323510665 Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Corticoids and Gestagens; Gestagen; Glucocorticoids; Isoprene Metabolism;
Cyp24a1 1,25-dihydroxyvitamin D(3) 24-hydroxylase, mitochondrial * 6753572
Cyp27a1 sterol 26-hydroxylase, mitochondrial 568905604 Steroid Metabolism: Cholesterol Synthesis; Zoosterols;
Cyp27b1 25-hydroxyvitamin D-1 alpha hydroxylase, mitochondrial * 568966604
Cyp2r1 vitamin D 25-hydroxylase 568950651 Steroid Metabolism: Cholesterol Synthesis; Zoosterols;
Cyp7a1 cholesterol 7-alpha-monooxygenase 31542445 Steroid Metabolism: Cholesterol Synthesis; Zoosterols;
Cyp7b1 25-hydroxycholesterol 7-alpha-hydroxylase 160707927 Steroid Metabolism: Cholesterol Synthesis; Zoosterols;
D2hgdh D-2-hydroxyglutarate dehydrogenase, mitochondrial * 1039730464
Dak bifunctional ATP-dependent dihydroxyacetone kinase/FAD-AMP lyase (cyclizing) 84781664 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm;
Dao D-amino-acid oxidase 556695486 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Urea Cycle; Citrate and Glyoxalate Cycle; Lipid Metabolism: Glyco- and Phospholipids; Glutamate Group of Amino Acids; Glyoxylate Cycle; Histidine Metabolism; Mesaconate Pathway; Urea Cycle;
Dars2 aspartate--tRNA ligase, mitochondrial * 568910677
Dbh dopamine beta-hydroxylase 110815861 Amino Acid Metabolism: Histidine; Histidine Metabolism; Vitamins, Co-Enzymes, and Hormones; Catecholamines;
Dbt lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial* 170172520
Dck deoxycytidine kinase 6681141 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Pyrimidine Metabolism;
Dctd deoxycytidylate deaminase isoform 2 568954869 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Pyrimidines; Pyrimidine Metabolism;
Dcxr L-xylulose reductase 568975430 Carbohydrate Metabolism: Pentoses and Pentose Cycle; Pentose Interconversions; Carbohydrates; Pentoses;
Ddah1 N(G),N(G)-dimethylarginine dimethylaminohydrolase 1* 38371755
Ddah2 N(G),N(G)-dimethylarginine dimethylaminohydrolase 2 * 569000983
Ddc aromatic-L-amino-acid decarboxylase isoform b 568969819 Amino Acid Metabolism: Histidine; Histidine Metabolism; Amino Acids; Aromatic amino acids; Catecholamines;
Decr1 2,4-dienoyl-CoA reductase, mitochondrial * 13385680
Decr2 peroxisomal 2,4-dienoyl-CoA reductase* 6753622
Dgat1 diacylglycerol O-acyltransferase 1 1039748163 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Lipid Metabolism; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Dgat2 diacylglycerol O-acyltransferase 2 16975490 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Lipid Metabolism; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Dgka diacylglycerol kinase alpha 1039732061 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Dgkb diacylglycerol kinase beta 83816899 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Dgkd diacylglycerol kinase delta isoform X4 1039728688 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Dgke diacylglycerol kinase, epsilon 64kDa 9506541 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Dgkg diacylglycerol kinase gamma 20149724 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Dgkh diacylglycerol kinase eta-like isoform X5 1039746398 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Dgki diacylglycerol kinase iota 1039775260 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Dgkk diacylglycerol kinase kappa-like 189491687 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Dgkq diacylglycerol kinase, theta 39841023 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Dgkz diacylglycerol kinase zeta 1039758719 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Dguok deoxyguanosine kinase, mitochondrial * 1039775175
Dhcr7 7-dehydrocholesterol reductase 755524057 Steroid Metabolism: Cholesterol Synthesis; Zoosterols;
Dhfr dihydrofolate reductase 7106289 Antibiotics: Penicillin, Cephalosporin; C1-Metabolism; One Carbon Pool; Folic Acid Metabolism;
Dhfrl1 dihydrofolate reductase, mitochondrial 307548863 Antibiotics: Penicillin, Cephalosporin; C1-Metabolism; One Carbon Pool; Folic Acid Metabolism;
Dhodh dihydroorotate dehydrogenase (quinone), mitochondrial precursor 9910194 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis;
Dhrs1 dehydrogenase/reductase SDR family member 1 31980844 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Dhrs2 dehydrogenase/reductase SDR family member 2, mitochondrial 755548910 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Dhrs3 short-chain dehydrogenase/reductase 3 6755380 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Dhrs4 dehydrogenase/reductase SDR family member 4 256220343 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Dhrs7b dehydrogenase/reductase SDR family member 7B * 285403538
Dhtkd1 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial 1039759799 Amino Acid Metabolism: Lysine; Citrate and Glyoxalate Cycle; Glyoxylate Cycle; Lysine Metabolism; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle;
Dlat dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex, mitochondrial 257796245 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Carbohydrates; Glycolysis in the Cytoplasm; TCA Cycle in the Mitochondrial Matrix;
Dld dihydrolipoyl dehydrogenase, mitochondrial precursor 31982856 Carbohydrate Metabolism: Pyruvate Turnover; Citrate and Glyoxalate Cycle; Anaplerotic Reactions; Glyoxylate Cycle; Carbohydrates; Glycolysis in the Cytoplasm;
Dlst dihydrolipoyllysine-residue succinyltransferase component of 2-oxoglutarate dehydrogenase complex, mitochondrial 1039742166 Citrate and Glyoxalate Cycle; Glyoxylate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Dmgdh dimethylglycine dehydrogenase, mitochondrial precursor 21311901 Lipid Metabolism: Glyco- and Phospholipids; Amino Acids; Amino acids;
Dnase1 deoxyribonuclease-1 precursor 568994587 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines;
Dnase2 deoxyribonuclease-2-alpha precursor 19924079 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines;
Dnase2b deoxyribonuclease-2-beta precursor 225543441 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines;
Dnmt1 DNA (cytosine-5)-methyltransferase 1 755528341 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Dnmt3a DNA (cytosine-5)-methyltransferase 3A isoform 1 568977472 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Dnmt3b DNA (cytosine-5)-methyltransferase 3B isoform X12 568915301 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Dolk dolichol kinase 29244058 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids;
Dpyd dihydropyrimidine dehydrogenase [NADP(+)] 755504833 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Pyrimidines; Pyrimidine Metabolism;
Dpys dihydropyrimidinase 257096000 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Pyrimidines; Pyrimidine Metabolism;
Dtymk thymidylate kinase 157785665 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Pyrimidines;
Dus2 tRNA-dihydrouridine(20) synthase [NAD(P)+]-like * 568957384
Dut deoxyuridine 5'-triphosphate nucleotidohydrolase isoform 2 227497222 Nucleotide Metabolism: Pyrimidines; Pyrimidines;
Ears2 glutamate--tRNA ligase, mitochondrial 568951240 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Ech1 delta(3,5)-Delta(2,4)-dienoyl-CoA isomerase, mitochondrial * 7949037
Echdc1 ethylmalonyl-CoA decarboxylase 568965529 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids;
Echdc2 enoyl-CoA hydratase domain-containing protein 2, mitochondrial 1039768218 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids;
Echdc3 enoyl-CoA hydratase domain-containing protein 3, mitochondrial precursor 31980955 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids;
Echs1 enoyl-CoA hydratase, mitochondrial precursor 29789289 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Lipid Metabolism: Fatty Acids; Branched Chain Amino Acids; Fatty Acid Oxidation; Sulfur Metabolism; Amino Acids; Amino acids; Lipid degradation; Lipid Metabolism;
Eci1 enoyl-CoA delta isomerase 1, mitochondrial * 31981810
Eci2 enoyl-CoA delta isomerase 2, mitochondrial * 160333193
Eci3 enoyl-CoA delta isomerase 3, peroxisomal * 755544356
Ehhadh enoyl-CoA hydratase/3,2-trans-enoyl-CoA isomerase 568996435 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Lipid Metabolism: Fatty Acids; Branched Chain Amino Acids; Fatty Acid Oxidation; Sulfur Metabolism; Amino Acids; Amino acids; Lipid degradation; Lipid Metabolism;
Elac1 zinc phosphodiesterase ELAC protein 1* 31981497
Elac2 zinc phosphodiesterase ELAC protein 2 * 1039738062
Endog endonuclease G, mitochondrial * 6679647
Eno1 alpha-enolase 1039766553 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Glycolysis and TCA Cycle;
Eno2 gamma-enolase 568940591 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Glycolysis and TCA Cycle;
Eno3 beta-enolase 443497949 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Glycolysis and TCA Cycle;
Eno4 enolase-like protein ENO4 569007187 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Glycolysis and TCA Cycle;
Enpp1 ectonucleotide pyrophosphatase/phosphodiesterase family member 1 568965121 Lipid Metabolism: Sphingolipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines; Lipids; Phospholipids;
Enpp2 ectonucleotide pyrophosphatase/phosphodiesterase family member 2 1039748453 Lipid Metabolism: Sphingolipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines; Lipids; Phospholipids;
Enpp3 ectonucleotide pyrophosphatase/phosphodiesterase family member 3 154240724 Lipid Metabolism: Sphingolipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines; Lipids; Phospholipids;
Enpp4 ectonucleotide pyrophosphatase/phosphodiesterase family member 4 isoform X6 1039753374 Lipid Metabolism: Sphingolipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines; Lipids; Phospholipids;
Enpp5 ectonucleotide pyrophosphatase/phosphodiesterase family member 5 precursor 1045559357 Lipid Metabolism: Sphingolipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines; Lipids; Phospholipids;
Enpp6 ectonucleotide pyrophosphatase/phosphodiesterase family member 6 precursor 28893409 Lipid Metabolism: Sphingolipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines; Lipids; Phospholipids;
Enpp7 ectonucleotide pyrophosphatase/phosphodiesterase family member 7 precursor 568973826 Lipid Metabolism: Sphingolipids; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines; Lipids; Phospholipids;
Entpd1 ectonucleoside triphosphate diphosphohydrolase 1 1039757103 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Entpd2 ectonucleoside triphosphate diphosphohydrolase 2 precursor 161484610 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Entpd3 ectonucleoside triphosphate diphosphohydrolase 3 255683318 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Entpd4 ectonucleoside triphosphate diphosphohydrolase 4 18093090 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Entpd5 ectonucleoside triphosphate diphosphohydrolase 5 precursor 554790267 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Entpd6 ectonucleoside triphosphate diphosphohydrolase 6 83921570 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Entpd7 ectonucleoside triphosphate diphosphohydrolase 7 82617566 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Entpd8 ectonucleoside triphosphate diphosphohydrolase 8 1039762003 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Ephx1 epoxide hydrolase 1 * 922304352
Ephx2 bifunctional epoxide hydrolase 2 isoform d* 406647884
Ephx3 epoxide hydrolase 3 * 755559060
Ephx4 epoxide hydrolase 4 * 568935875
Eprs bifunctional aminoacyl-tRNA synthetase 1039727247 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Ept1 ethanolaminephosphotransferase 1 111119005 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Phospholipids;
Eri1 3'-5' exoribonuclease 1* 165905605
Eri2 ERI1 exoribonuclease 2 * 1039779925
Eri3 ERI1 exoribonuclease 3 1* 1039766609
Etfa electron transfer flavoprotein subunit alpha, mitochondrial* 227500281
Etfdh electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial precursor 254588014 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Ethe1 persulfide dioxygenase ETHE1, mitochondrial * 1039779611
Etnk1 ethanolamine kinase 1 568944321 Lipid Metabolism: Glyco- and Phospholipids; Phospholipids;
Etnk2 ethanolamine kinase 2 568908608 Lipid Metabolism: Glyco- and Phospholipids; Phospholipids;
Exog nuclease EXOG, mitochondrial * 755531806
Fah fumarylacetoacetase 240120112 Amino Acid Metabolism: Histidine; Histidine Metabolism; Carbohydrates; Glycolysis in the Cytoplasm;
Fahd1 acylpyruvase FAHD1, mitochondrial* 12963697
Fahd2a fumarylacetoacetate hydrolase domain-containing protein 2A * 568918221
Fan1 fanconi-associated nuclease 1 257467664 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines;
Fars2 phenylalanine--tRNA ligase, mitochondrial * 1039744151
Fasn fatty acid synthase 93102409 Lipid Metabolism: Fatty Acids; Fatty Acid Synthesis; Carbohydrates; Lipids; Glycolysis in the Cytoplasm; Lipid biosynthesis; Lipid Metabolism;
Fbp1 fructose-1,6-bisphosphatase 1 755545286 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation; Pentose Phosphate Pathways;
Fbp2 fructose-1,6-bisphosphatase isozyme 2 122937183 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation; Pentose Phosphate Pathways;
Fbp3 fructose-1,6-bisphosphatase 1 9506589 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation; Pentose Phosphate Pathways;
Fdft1 squalene synthase 1039745489 Lipid Metabolism: Carotenoids and Isoprenoids; Isoprenoids; Lipids; Steroids; Products of Isoprene Metabolism;
Fdps farnesyl pyrophosphate synthase 359279938 Lipid Metabolism: Carotenoids and Isoprenoids; Isoprenoids; Lipids; Steroids; Isoprene Metabolism; Products of Isoprene Metabolism;
Fdxr NADPH:adrenodoxin oxidoreductase, mitochondrial * 6679767
Fech ferrochelatase, mitochondrial 1039755604 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Vitamins, Co-Enzymes, and Hormones; Porphyrins; Heme Metabolism;
Fh fumarate hydratase, mitochondrial precursor 158186722 Citrate and Glyoxalate Cycle; Glyoxylate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Deamination of Amino Acids: The Urea Cycle; Glycolysis and TCA Cycle;
Fh1 fumarate hydratase, mitochondrial * 226823367
Fhit bis(5'-adenosyl)-triphosphatase * 1039745502
Fkbp10 peptidyl-prolyl cis-trans isomerase FKBP10 * 254939534
Fkbp11 peptidyl-prolyl cis-trans isomerase FKBP11 * 15277331
Fkbp14 peptidyl-prolyl cis-trans isomerase FKBP14 * 23956366
Fkbp15 FK506-binding protein 15* 227116320
Fkbp2 peptidyl-prolyl cis-trans isomerase FKBP2 * 261824055
Fkbp3 peptidyl-prolyl cis-trans isomerase FKBP3* 7305061
Fkbp4 peptidyl-prolyl cis-trans isomerase FKBP4* 6753882
Fkbp5 peptidyl-prolyl cis-trans isomerase FKBP5* 6753884
Fkbp6 inactive peptidyl-prolyl cis-trans isomerase FKBP6 * 1039772986
Fkbp7 peptidyl-prolyl cis-trans isomerase FKBP7 * 6806909
Fkbp8 peptidyl-prolyl cis-trans isomerase FKBP8 * 313851007
Fkbp9 peptidyl-prolyl cis-trans isomerase FKBP9 * 172072617
Flad1 FAD synthase* 89337262
Fnta protein farnesyltransferase/geranylgeranyltransferase type-1 subunit alpha 6679821 Carbohydrates; Polysaccharides;
Foxred1 FAD-dependent oxidoreductase domain-containing protein 1 * 1039792910
Foxred2 FAD-dependent oxidoreductase domain-containing protein 2 * 1039748848
Fpgs folylpolyglutamate synthase, mitochondrial * 1039759070
Ftcd formimidoyltransferase-cyclodeaminase 18252784 Amino Acid Metabolism: Histidine; C1-Metabolism; Histidine Metabolism; One Carbon Pool; Folic Acid Metabolism; Folic Acid Reactions;
Fth1 ferritin heavy chain 6753912 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
Ftmt ferritin, mitochondrial 247270151 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
Fut1 galactoside 2-alpha-L-fucosyltransferase 1 431822410 Carbohydrates; Polysaccharides;
Fut10 alpha-(1,3)-fucosyltransferase 10 568953898 Carbohydrates; Polysaccharides;
Fut11 alpha-(1,3)-fucosyltransferase 11 precursor 58037305 Carbohydrates; Polysaccharides;
Fut2 galactoside 2-alpha-L-fucosyltransferase 2 431822426 Carbohydrates; Polysaccharides;
Fut3 galactoside 3(4)-L-fucosyltransferase 4503809 Carbohydrates; Polysaccharides;
Fut4 alpha-(1,3)-fucosyltransferase 4 6753920 Carbohydrates; Polysaccharides;
Fut5 alpha-(1,3)-fucosyltransferase 5 52485799 Carbohydrates; Polysaccharides;
Fut6 alpha-(1,3)-fucosyltransferase 6 4503815 Carbohydrates; Polysaccharides;
Fut7 alpha-(1,3)-fucosyltransferase 755497180 Carbohydrates; Polysaccharides;
Fut8 alpha-(1,6)-fucosyltransferase 357933610 Carbohydrates; Polysaccharides;
Fut9 alpha-(1,3)-fucosyltransferase 9 6753922 Carbohydrates; Polysaccharides;
Fxn frataxin, mitochondrial 6679863 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
G6pc glucose-6-phosphatase 31982353 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation;
G6pc2 glucose-6-phosphatase 2 isoform 3 578888065 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation;
G6pc3 glucose-6-phosphatase 3 47271524 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation;
G6pd glucose-6-phosphate 1-dehydrogenase 8393381 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Pentose Phosphate Pathways;
G6pd2 glucose-6-phosphate 1-dehydrogenase 2 227330582 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Pentose Phosphate Pathways;
G6pdx glucose-6-phosphate 1-dehydrogenase X 6996917 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Pentose Phosphate Pathways;
Gaa lysosomal alpha-glucosidase precursor 226693369 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Gad1 glutamate decarboxylase 1 1039759088 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Glutamate Decarboxylation Pathway; Amino Acids; Amino acids;
Gad2 glutamate decarboxylase 2 755497184 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Glutamate Decarboxylation Pathway; Amino Acids; Amino acids;
Gadl1 glutamate decarboxylase-like protein 1-like 197382957 Amino Acids; Amino acids;
Gal3st1 galactosylceramide sulfotransferase isoform X3 755536478 C1-Metabolism; One Carbon Pool; Folic Acid Metabolism; Folic Acid Reactions;
Gal3st2 galactose-3-O-sulfotransferase 2-like 224922779 C1-Metabolism; One Carbon Pool; Folic Acid Metabolism; Folic Acid Reactions;
Gal3st3 galactose-3-O-sulfotransferase 3 85701542 C1-Metabolism; One Carbon Pool; Folic Acid Metabolism; Folic Acid Reactions;
Gal3st4 galactose-3-O-sulfotransferase 4 1039771821 C1-Metabolism; One Carbon Pool; Folic Acid Metabolism; Folic Acid Reactions;
Galc galactocerebrosidase precursor 1039739775 Lipids; Phospholipids;
Gale UDP-glucose 4-epimerase 1039768859 Carbohydrate Metabolism: Nucleotide Sugars; Carbohydrates; Polysaccharides;
Galk1 galactokinase 93102413 Carbohydrate Metabolism: Di-and Polysaccharides; Carbohydrates; Polysaccharides;
Galk2 N-acetylgalactosamine kinase 755500520 Carbohydrate Metabolism: Di-and Polysaccharides; Carbohydrates; Polysaccharides;
Galt galactose-1-phosphate uridylyltransferase 700274118 Carbohydrate Metabolism: Nucleotide Sugars; Carbohydrates; Polysaccharides;
Gamt guanidinoacetate N-methyltransferase 6753944 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids;
Ganc neutral alpha-glucosidase C 124487339 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Gapdh glyceraldehyde-3-phosphate dehydrogenase 1039774280 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Glycolysis and TCA Cycle;
Gapdhs glyceraldehyde-3-phosphate dehydrogenase, testis-specific 755519097 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Glycolysis and TCA Cycle;
Gars glycine--tRNA ligase 93102417 Citrate and Glyoxalate Cycle; Glyoxylate Cycle;
Gart phosphoribosylamine--glycine ligase 568997285 C1-Metabolism; Carbohydrate Metabolism: Pentoses and Pentose Cycle; Nucleotide Metabolism: Purines; One Carbon Pool; Pentose Interconversions; Purine Biosynthesis; Amino Acids; Purines and Pyrimidines; Amino acids; Purines; Folic Acid Metabolism; Folic Acid Reactions; Purine Metabolism;
Gatc glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial* 47059159
Gatm glycine amidinotransferase, mitochondrial precursor 13385454 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids;
Gba glucosylceramidase precursor 568921790 Carbohydrate Metabolism: Di-and Polysaccharides; Lipid Metabolism: Sphingolipids;
Gba2 non-lysosomal glucosylceramidase 568926511 Carbohydrate Metabolism: Di-and Polysaccharides; Lipid Metabolism: Sphingolipids;
Gba3 glucosidase, beta, acid 3 isoform X3 564383889 Carbohydrate Metabolism: Di-and Polysaccharides; Lipid Metabolism: Sphingolipids;
Gbe1 1,4-alpha-glucan-branching enzyme 17975508 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Gcdh glutaryl-CoA dehydrogenase, mitochondrial 390190197 Amino Acid Metabolism: Lysine; Lysine Metabolism; Amino Acids; Amino acids; Lipid degradation;
Gch1 GTP cyclohydrolase 1 precursor 6679967 Antibiotics: Penicillin, Cephalosporin; Pterine Biosynthesis;
Gck glucokinase isoform 3 565671715 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm;
Gclc glutamate--cysteine ligase catalytic subunit 33468897 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids;
Gclm glutamate--cysteine ligase regulatory subunit 6680019 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids;
Gcsh glycine cleavage system H protein, mitochondrial * 13386066
Gda guanine deaminase 1039757181 Nucleotide Metabolism: Purines; Purines and Pyrimidines; Purines; Purine Metabolism;
Gfpt1 glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 7305085 Carbohydrate Metabolism: Amino Sugar Derivatives; Carbohydrates; Glycolysis in the Cytoplasm;
Gfpt2 glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 7305087 Carbohydrate Metabolism: Amino Sugar Derivatives; Carbohydrates; Glycolysis in the Cytoplasm;
Ggps1 geranylgeranyl pyrophosphate synthase 1063759744 Lipid Metabolism: Carotenoids and Isoprenoids; Isoprenoids; Lipids; Steroids; Isoprene Metabolism; Products of Isoprene Metabolism;
Gk glycerol kinase 1061975060 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Lipid biosynthesis; Gluconeogenesis and Glycolysis;
Gk2 glycerol kinase 2 6754000 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Lipid biosynthesis; Gluconeogenesis and Glycolysis;
Gk3p putative glycerol kinase 3 215277039 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Lipid biosynthesis; Gluconeogenesis and Glycolysis;
Gk5 putative glycerol kinase 5-like isoform X3 568961414 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Lipid biosynthesis; Gluconeogenesis and Glycolysis;
Glb1 beta-galactosidase precursor 6753190 Carbohydrate Metabolism: Di-and Polysaccharides; Carbohydrate Metabolism: Pentoses and Pentose Cycle; Pentose Interconversions; Carbohydrates; Pentoses; Polysaccharides;
Glb1l2 beta-galactosidase-1-like protein 2 568959444 Carbohydrate Metabolism: Di-and Polysaccharides; Carbohydrates; Polysaccharides;
Gldc glycine dehydrogenase [decarboxylating], mitochondrial 20070408 C1-Metabolism; One Carbon Pool; Amino Acids; Amino acids; Folic Acid Metabolism; Folic Acid Reactions;
Glo1 lactoylglutathione lyase 165932333 Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Porphyrins;
Gls glutaminase kidney isoform, mitochondrial isoform a 1039727595 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids; Deamination of Amino Acids: The Urea Cycle;
Gls2 glutaminase liver isoform, mitochondrial isoform 2 552953810 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids; Deamination of Amino Acids: The Urea Cycle;
Glud1 glutamate dehydrogenase 1, mitochondrial precursor 6680027 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Deamination of Amino Acids: The Urea Cycle; Isoprene Metabolism;
Glud2 glutamate dehydrogenase 2, mitochondrial precursor 31377775 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Deamination of Amino Acids: The Urea Cycle; Isoprene Metabolism;
Glul glutamine synthetase 31982332 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Glutamate Decarboxylation Pathway; Mesaconate Pathway; Amino Acids; Amino acids; Deamination of Amino Acids: The Urea Cycle;
Glyat glycine N-acyltransferase* 22122359
Glyctk glycerate kinase 755531314 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm;
Gmds GDP-mannose 4,6 dehydratase 22122523 Carbohydrates; Polysaccharides;
Gmpr GMP reductase 1 1039743937 Purine Metabolism;
Gmpr2 GMP reductase 2 755547551 Purine Metabolism;
Gmps GMP synthase [glutamine-hydrolyzing] 85861218 Nucleotide Metabolism: Purines; Purine Metabolism;
Gne bifunctional UDP-N-acetylglucosamine 2-epimerase/N-acetylmannosamine kinase 298676517 Carbohydrate Metabolism: Amino Sugar Derivatives; Amino Sugars; Carbohydrates; Polysaccharides;
Gnmt glycine N-methyltransferase 6754026 Amino Acids; Amino acids;
Gnpda1 glucosamine-6-phosphate isomerase 1 188219582 Carbohydrate Metabolism: Amino Sugar Derivatives;
Gnpda2 glucosamine-6-phosphate isomerase 2 755511672 Carbohydrate Metabolism: Amino Sugar Derivatives;
Gnpnat1 glucosamine 6-phosphate N-acetyltransferase 755548584 Carbohydrate Metabolism: Amino Sugar Derivatives; Carbohydrates; Polysaccharides;
Got1 aspartate aminotransferase, cytoplasmic 160298209 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Amino Acid Metabolism: Urea Cycle; Citrate and Glyoxalate Cycle; Glyoxylate Cycle; Mesaconate Pathway; Sulfur Metabolism; Urea Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Deamination of Amino Acids: The Urea Cycle;
Got1l1 putative aspartate aminotransferase, cytoplasmic 2 755525112 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Amino Acid Metabolism: Urea Cycle; Citrate and Glyoxalate Cycle; Glyoxylate Cycle; Mesaconate Pathway; Sulfur Metabolism; Urea Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Deamination of Amino Acids: The Urea Cycle;
Got2 aspartate aminotransferase, mitochondrial 6754036 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Amino Acid Metabolism: Urea Cycle; Citrate and Glyoxalate Cycle; Nucleotide Metabolism: NAD, NADP; Glyoxylate Cycle; Mesaconate Pathway; Sulfur Metabolism; Urea Cycle; Amino Acids; Carbohydrates; Amino acids; TCA Cycle in the Mitochondrial Matrix; Deamination of Amino Acids: The Urea Cycle;
Gpam glycerol-3-phosphate acyltransferase 1, mitochondrial 755562794 Carbohydrate Metabolism: Pentoses and Pentose Cycle; Lipid Metabolism: Fatty Acids; Lipid Metabolism; Pentose Cycle; Carbohydrates; Lipids; Glycolysis in the Cytoplasm; Lipid biosynthesis; Lipid Metabolism; Purine Metabolism;
Gpat2 glycerol-3-phosphate acyltransferase 2, mitochondrial 1039759877 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Gpcpd1 glycerophosphocholine phosphodiesterase GPCPD1 1039762131 Lipid Metabolism: Glyco- and Phospholipids; Lipids; Phospholipids;
Gpd1 glycerol-3-phosphate dehydrogenase [NAD(+)], cytoplasmic 6753966 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Lipid Metabolism;
Gpd1l glycerol-3-phosphate dehydrogenase 1-like protein 257467604 Lipid Metabolism;
Gpd2 glycerol-3-phosphate dehydrogenase, mitochondrial precursor 224922806 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Lipid Metabolism;
Gpi glucose-6-phosphate isomerase 46485440 Carbohydrate Metabolism: Amino Sugar Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Glycolysis and TCA Cycle; Pentose Phosphate Pathways;
Gpi1 glucose-6-phosphate isomerase* 254553458
Gpt alanine aminotransferase 1 33413404 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Carbohydrate Metabolism: Pyruvate Turnover; Citrate and Glyoxalate Cycle; Anaplerotic Reactions; Citrate Cycle; Mesaconate Pathway; Amino Acids; Amino acids; Deamination of Amino Acids: The Urea Cycle;
Gpt2 alanine aminotransferase 2 568955903 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Mesaconate Pathway; Amino Acids; Amino acids; Deamination of Amino Acids: The Urea Cycle;
Gpx1 glutathione peroxidase 1 isoform 3* 1043678444
Gpx2 glutathione peroxidase 2* 145275168
Gpx3 glutathione peroxidase 3 * 1049329726
Gpx4 phospholipid hydroperoxide glutathione peroxidase, mitochondrial * 90903235
Gpx5 epididymal secretory glutathione peroxidase * 171543846
Gpx6 glutathione peroxidase 6 * 146260278
Gpx7 glutathione peroxidase 7 * 13195626
Gpx8 probable glutathione peroxidase 8* 21312336
Grhpr glyoxylate reductase/hydroxypyruvate reductase 919185150 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Citrate and Glyoxalate Cycle; Glycolysis; Glyoxylate Cycle; Phospholipids;
Gsr glutathione reductase 160298213 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gss glutathione synthetase 568915502 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids;
Gsta1 glutathione S-transferase alpha-3 154350202 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gsta2 glutathione S-transferase alpha-1 568960750 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gsta3 glutathione S-transferase alpha-5 isoform 2 568786343 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gsta4 glutathione S-transferase alpha-4 160298217 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gsta5 glutathione S-transferase alpha-2 58331251 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gsta6 glutathione S-transferase A6 66730521 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstk1 glutathione S-transferase kappa 1 21313138 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstm1 glutathione S-transferase Mu 1 6754084 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstm2 glutathione S-transferase Mu 2 6680121 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstm3 glutathione S-transferase Mu 3 33468899 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstm4 glutathione S-transferase Mu 4 238018082 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstm5 glutathione S-transferase Mu 5 6754086 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstm6 glutathione S-transferase Mu 6 113680506 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstm7 glutathione S-transferase Yb-3 568923830 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gsto1 glutathione S-transferase omega-1 6754090 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gsto2 glutathione S-transferase omega-2 313151238 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstp1 glutathione S-transferase P 10092608 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstp2 glutathione S-transferase P 2 32401425 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstt1 glutathione S-transferase theta-1 160298219 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstt2 glutathione S-transferase theta-2 158081796 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstt2b glutathione S-transferase theta-2B 124249394 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstt3 glutathione S-transferase, theta 3 21536248 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstt4 glutathione S-transferase theta-4 294610650 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstya glutathione S-transferase A1 121712 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Gstz1 maleylacetoacetate isomerase 568978819 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Amino Acid Metabolism: Histidine; Histidine Metabolism; Mesaconate Pathway; Amino Acids; Aromatic amino acids;
Guk1 guanylate kinase 568971699 Nucleotide Metabolism: Purines; Purines and Pyrimidines; Purines; Purine Metabolism;
Guk2 guanylate kinase 2 Nucleotide Metabolism: Purines; Purines and Pyrimidines; Purines; Purine Metabolism;
Gulo L-gulonolactone oxidase 568987791 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrates; Hexoses;
Gusb beta-glucuronidase precursor 755514254 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives;
Gys1 glycogen [starch] synthase, muscle 31560022 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Carbohydrates; Polysaccharides;
Gys2 glycogen [starch] synthase, liver 188035875 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Carbohydrates; Polysaccharides;
H2-Ke6 estradiol 17-beta-dehydrogenase 8 157951743 Steroid Metabolism: Androgens and Estrogens; Estrogens;
H6pd glucose 1-dehydrogenase 568930405 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Isoprene Metabolism;
Haao 3-hydroxyanthranilate 3,4-dioxygenase 568998606 Nucleotide Metabolism: NAD, NADP; Amino Acids; Aromatic amino acids;
Hadh hydroxyacyl-coenzyme A dehydrogenase, mitochondrial precursor 111038118 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Lipid Metabolism: Fatty Acids; Branched Chain Amino Acids; Fatty Acid Oxidation; Sulfur Metabolism; Amino Acids; Lipids; Amino acids; Lipid degradation; Lipid Metabolism;
Hadha long-chain enoyl-CoA hydratase 33859811 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Lipid Metabolism: Fatty Acids; Branched Chain Amino Acids; Fatty Acid Oxidation; Sulfur Metabolism; Amino Acids; Amino acids; Lipid degradation; Lipid Metabolism;
Hadhb 3-ketoacyl-CoA thiolase 1039771204 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Fatty Acids; Branched Chain Amino Acids; Fatty Acid Oxidation; Amino Acids; Amino acids; Lipid degradation; Lipid Metabolism;
Hagh hydroxyacylglutathione hydrolase, mitochondrial precursor 568999019 Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Porphyrins;
Hal histidine ammonia-lyase 6754152 Amino Acid Metabolism: Histidine; Histidine Metabolism; Amino Acids; Amino acids;
Hao1 hydroxyacid oxidase 1 6754156 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Citrate and Glyoxalate Cycle; Glyoxylate Cycle;
Hao2 hydroxyacid oxidase 2 755504120 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Citrate and Glyoxalate Cycle; Glyoxylate Cycle;
Hars2 probable histidine--tRNA ligase, mitochondrial * 755561263
Hccs holocytochrome c synthase 1061975092 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
Hdc histidine decarboxylase 568915509 Amino Acid Metabolism: Histidine; Histidine Metabolism; Amino Acids; Amino acids;
Hdhd2 haloacid dehalogenase-like hydrolase domain-containing protein 2 * 85861235
Hdhd3 haloacid dehalogenase-like hydrolase domain-containing protein 3* 21312204
Hemk1 hemK methyltransferase family member 1 * 1039794107
Hgd homogentisate 1,2-dioxygenase 240120123 Amino Acid Metabolism: Histidine; Histidine Metabolism;
Hibadh 3-hydroxyisobutyrate dehydrogenase, mitochondrial precursor 21704140 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids; Amino Acids; Amino acids;
Hibch 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial 22122625 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Branched Chain Amino Acids; Sulfur Metabolism; Amino Acids; Amino acids;
Hk1 hexokinase-1 225735584 Carbohydrate Metabolism: Amino Sugar Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation; Glycolysis and TCA Cycle;
Hk2 hexokinase-2 7305143 Carbohydrate Metabolism: Amino Sugar Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation; Glycolysis and TCA Cycle;
Hk3 hexokinase-3 329755312 Carbohydrate Metabolism: Amino Sugar Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation; Glycolysis and TCA Cycle;
Hkdc1 putative hexokinase HKDC1 755534346 Carbohydrate Metabolism: Amino Sugar Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation; Glycolysis and TCA Cycle;
Hmbs porphobilinogen deaminase 159110431 Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Porphyrins; Vitamins, Co-Enzymes, and Hormones; Porphyrins; Heme Metabolism;
Hmgcl hydroxymethylglutaryl-CoA lyase, mitochondrial precursor 1039766668 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane; Lipid Metabolism;
Hmgcll1 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic 755529910 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane; Lipid Metabolism;
Hmgcr 3-hydroxy-3-methylglutaryl-coenzyme A reductase 160358778 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Lipids; Phospholipids; Isoprene Metabolism; Lipid Metabolism;
Hmgcs1 hydroxymethylglutaryl-CoA synthase, cytoplasmic 568984319 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Ketone Bodies; Lipids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism;
Hmgcs2 hydroxymethylglutaryl-CoA synthase, mitochondrial precursor 31560689 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Ketone Bodies; Lipids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism;
Hmox1 heme oxygenase 1 6754212 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
Hmox2 heme oxygenase 2 755553196 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
Hmox2-ps1 heme oxygenase (decycling) 2, pseudogene 1 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
Hnmt histamine N-methyltransferase 17978276 Amino Acid Metabolism: Histidine; Histidine Metabolism;
Hoga1 4-hydroxy-2-oxoglutarate aldolase, mitochondrial 13385656 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids;
Hpd 4-hydroxyphenylpyruvate dioxygenase 33859486 Amino Acid Metabolism: Histidine; Histidine Metabolism; Amino Acids; Aromatic amino acids;
Hpgds hematopoietic prostaglandin D synthase 568942444 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Hprt1 hypoxanthine-guanine phosphoribosyltransferase 392356055 Nucleotide Metabolism: Purines; Purine Metabolism;
Hsd11b1 corticosteroid 11-beta-dehydrogenase isozyme 1 568911950 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Glucocorticoids; Mineralcorticoids;
Hsd11b2 corticosteroid 11-beta-dehydrogenase isozyme 2 133778913 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Glucocorticoids; Mineralcorticoids;
Hsd17b1 estradiol 17-beta-dehydrogenase 1 6754248 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Androgens and Estrogens; Androgens; Branched Chain Amino Acids; Carotenoids; Estrogens; Fatty Acid Oxidation; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Hsd17b10 3-hydroxyacyl-CoA dehydrogenase type-2 61888838 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Androgens and Estrogens; Androgens; Branched Chain Amino Acids; Carotenoids; Estrogens; Fatty Acid Oxidation; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Hsd17b11 estradiol 17-beta-dehydrogenase 11 precursor 16716597 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Androgens and Estrogens; Androgens; Branched Chain Amino Acids; Carotenoids; Estrogens; Fatty Acid Oxidation; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Hsd17b12 estradiol 17-beta-dehydrogenase 12 9789991 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Androgens and Estrogens; Androgens; Branched Chain Amino Acids; Carotenoids; Estrogens; Fatty Acid Oxidation; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Hsd17b13 17-beta-hydroxysteroid dehydrogenase 13 precursor 254553342 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Androgens and Estrogens; Androgens; Branched Chain Amino Acids; Carotenoids; Estrogens; Fatty Acid Oxidation; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Hsd17b14 17-beta-hydroxysteroid dehydrogenase 14 755521221 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Androgens and Estrogens; Androgens; Branched Chain Amino Acids; Carotenoids; Estrogens; Fatty Acid Oxidation; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Hsd17b2 estradiol 17-beta-dehydrogenase 2 568956196 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Androgens and Estrogens; Androgens; Branched Chain Amino Acids; Carotenoids; Estrogens; Fatty Acid Oxidation; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Hsd17b3 testosterone 17-beta-dehydrogenase 3 568983060 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Androgens and Estrogens; Androgens; Branched Chain Amino Acids; Carotenoids; Estrogens; Fatty Acid Oxidation; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Hsd17b4 17-beta-hydroxysteroid dehydrogenase 4 31982273 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Androgens and Estrogens; Androgens; Branched Chain Amino Acids; Carotenoids; Estrogens; Fatty Acid Oxidation; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Hsd17b5 aldo-keto reductase family 1, member C1 76096330 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Androgens and Estrogens; Androgens; Branched Chain Amino Acids; Carotenoids; Estrogens; Fatty Acid Oxidation; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Hsd17b6 17-beta-hydroxysteroid dehydrogenase type 6 7305165 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Androgens and Estrogens; Androgens; Branched Chain Amino Acids; Carotenoids; Estrogens; Fatty Acid Oxidation; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Hsd17b7 3-keto-steroid reductase 1039727652 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Androgens and Estrogens; Androgens; Branched Chain Amino Acids; Carotenoids; Estrogens; Fatty Acid Oxidation; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Hsd17b8 estradiol 17-beta-dehydrogenase 8 47087119 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Androgens and Estrogens; Androgens; Branched Chain Amino Acids; Carotenoids; Estrogens; Fatty Acid Oxidation; Amino Acids; Vitamins, Co-Enzymes, and Hormones; Amino acids; Isoprenoids; Lipid degradation; Isoprene Metabolism; Lipid Metabolism; Products of Isoprene Metabolism;
Hsd3b 3 beta-hydroxysteroid dehydrogenase/Delta 5-->4-isomerase type 2 110835753 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Gestagen; Zoosterols; Isoprene Metabolism;
Hsd3b1 3 beta-hydroxysteroid dehydrogenase/Delta 5-->4-isomerase type 1 568921871 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Gestagen; Zoosterols; Isoprene Metabolism;
Hsd3b2 3 beta-hydroxysteroid dehydrogenase/Delta 5-->4-isomerase type 2 755503388 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Gestagen; Zoosterols; Isoprene Metabolism;
Hsd3b3 3 beta-hydroxysteroid dehydrogenase/Delta 5-->4-isomerase type 3 isoform 1 1039763827 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Gestagen; Zoosterols; Isoprene Metabolism;
Hsd3b4 3 beta-hydroxysteroid dehydrogenase type 4 1039763831 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Gestagen; Zoosterols; Isoprene Metabolism;
Hsd3b5 3 beta-hydroxysteroid dehydrogenase type 5 113680667 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Gestagen; Zoosterols; Isoprene Metabolism;
Hsd3b6 3 beta-hydroxysteroid dehydrogenase/Delta 5-->4-isomerase type 4 162461883 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Gestagen; Zoosterols; Isoprene Metabolism;
Hsd3b7 3 beta-hydroxysteroid dehydrogenase type 7 1039776832 Steroid Metabolism: Androgens and Estrogens; Steroid Metabolism: Cholesterol Synthesis; Steroid Metabolism: Mineralocorticoids and Glucocorticoids; Androgens; Gestagen; Zoosterols; Isoprene Metabolism;
Hsdl1 inactive hydroxysteroid dehydrogenase-like protein 1 * 568957633
Hsdl2 hydroxysteroid dehydrogenase-like protein 2 * 125656150
Htatip2 oxidoreductase HTATIP2 * 568948093
Hykk aminoglycoside phosphotransferase domain-containing protein 1 171184418 Amino Acid Metabolism: Lysine; Lysine Metabolism;
Iars isoleucyl-tRNA synthetase, cytoplasmic isoform X4 568982293 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids;
Iars2 isoleucine--tRNA ligase, mitochondrial 38490690 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids;
Ide insulin-degrading enzyme* 459352741
Idh1 isocitrate dehydrogenase [NADP] cytoplasmic 162417977 Citrate and Glyoxalate Cycle; Citrate Cycle;
Idh2 isocitrate dehydrogenase [NADP], mitochondrial precursor 568947926 Citrate and Glyoxalate Cycle; Citrate Cycle;
Idh3a isocitrate dehydrogenase [NAD] subunit alpha, mitochondrial precursor 18250284 Citrate and Glyoxalate Cycle; Citrate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle;
Idh3B isocitrate dehydrogenase [NAD] subunit beta, mitochondrial precursor 568915592 Citrate and Glyoxalate Cycle; Citrate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle;
Idh3g isocitrate dehydrogenase [NAD] subunit gamma 1, mitochondrial precursor 1039796369 Citrate and Glyoxalate Cycle; Citrate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle;
Idi1 isopentenyl-diphosphate Delta-isomerase 1 281604088 Lipid Metabolism: Carotenoids and Isoprenoids; Isoprenoids; Products of Isoprene Metabolism;
Idi2 isopentenyl-diphosphate delta isomerase 2 28893215 Lipid Metabolism: Carotenoids and Isoprenoids; Isoprenoids; Products of Isoprene Metabolism;
Idnk gluconokinase 114205446 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis;
Il4i1 L-amino-acid oxidase precursor 254553434 Amino Acid Metabolism: Histidine; Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids; Histidine Metabolism;
Impa1 inositol monophosphatase 1 568920615 Carbohydrate Metabolism: Inositol; Inositol Metabolism; Carbohydrates; Hexoses;
Impa2 inositol monophosphatase 2 16716595 Carbohydrate Metabolism: Inositol; Inositol Metabolism; Carbohydrates; Hexoses;
Impad1 inositol monophosphatase 3 29244210 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Carbohydrate Metabolism: Inositol; Inositol Metabolism; Sulfur Metabolism; Carbohydrates; Hexoses;
Impdh1 inosine-5'-monophosphate dehydrogenase 1 755515386 Nucleotide Metabolism: Purines; Purines and Pyrimidines; Purines; Purine Metabolism;
Impdh2 inosine-5'-monophosphate dehydrogenase 2 568962960 Nucleotide Metabolism: Purines; Purines and Pyrimidines; Purines; Purine Metabolism;
Isoc2a isochorismatase domain-containing protein 2A * 197333728
Isyna1 inositol-3-phosphate synthase 1 12963757 Carbohydrate Metabolism: Inositol; Inositol Metabolism; Carbohydrates; Hexoses;
Ivd isovaleryl-CoA dehydrogenase, mitochondrial precursor 568917869 Amino Acids; Amino acids;
Jmjd4 jmjC domain-containing protein 4 568972434 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Prostaglandins, Thromboxanes, and Leucotrienes;
Jmjd6 bifunctional arginine demethylase and lysyl-hydroxylase JMJD6 125988379 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Prostaglandins, Thromboxanes, and Leucotrienes;
Jmjd7 jmjC domain-containing protein 7 167860141 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Prostaglandins, Thromboxanes, and Leucotrienes;
Jmjd8 jmjC domain-containing protein 8 precursor 254910999 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Prostaglandins, Thromboxanes, and Leucotrienes;
Kars lysine--tRNA ligase 1039791051 Amino Acid Metabolism: Lysine; Lysine Metabolism;
Kat3 kynurenine--oxoglutarate transaminase 3 109465653 Nucleotide Metabolism: NAD, NADP;
Kdsr 3-ketodihydrosphingosine reductase 941355887 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Khk ketohexokinase 568933797 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Hexoses;
Kmo kynurenine 3-monooxygenase 19527030 Nucleotide Metabolism: NAD, NADP; Amino Acids; Aromatic amino acids;
Kynu kynureninase 755497893 Nucleotide Metabolism: NAD, NADP; Amino Acids; Aromatic amino acids;
L2hgdh L-2-hydroxyglutarate dehydrogenase, mitochondrial 21703884 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Citrate and Glyoxalate Cycle; Citrate Cycle;
Lactb serine beta-lactamase-like protein LACTB, mitochondrial * 568962317
Lactb2 endoribonuclease LACTB2* 21703764
Lars leucyl-tRNA synthetase, cytoplasmic 120537241 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids;
Lars2 leucyl-tRNA synthetase, mitochondrial 1039791812 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids;
Lclat1 lysocardiolipin acyltransferase 1 755556528 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Ldha L-lactate dehydrogenase A chain 6754524 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Sulfur Metabolism; Amino Acids; Amino acids; Gluconeogenesis and Glycolysis;
Ldhal6a L-lactate dehydrogenase A-like 6A 221136809 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Sulfur Metabolism; Amino Acids; Amino acids; Gluconeogenesis and Glycolysis;
Ldhal6b L-lactate dehydrogenase A-like 6B 30425048 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Sulfur Metabolism; Amino Acids; Amino acids; Gluconeogenesis and Glycolysis;
Ldhb L-lactate dehydrogenase B chain 938085832 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Sulfur Metabolism; Amino Acids; Amino acids; Gluconeogenesis and Glycolysis;
Ldhc L-lactate dehydrogenase C chain 568947440 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Sulfur Metabolism; Amino Acids; Amino acids; Gluconeogenesis and Glycolysis;
Ldhd D-lactate dehydrogenase, mitochondrial isoform X1 34328379 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Sulfur Metabolism; Amino Acids; Amino acids; Gluconeogenesis and Glycolysis;
Lhpp phospholysine phosphohistidine inorganic pyrophosphate phosphatase 568951597 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Lias lipoyl synthase, mitochondrial * 568934724
Lipa lysosomal acid lipase/cholesteryl ester hydrolase precursor 162287343 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Steroid Metabolism: Cholesterol Synthesis; Carotenoids; Fatty Acid Oxidation; Zoosterols; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Lipc hepatic triacylglycerol lipase precursor 568960759 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Lipf gastric triacylglycerol lipase precursor 1039758117 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Lipg endothelial lipase precursor 188219561 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Lipt1 lipoyltransferase 1, mitochondrial * 568906764
Lipt2 putative lipoyltransferase 2, mitochondrial* 229577004
Lpcat1 lysophosphatidylcholine acyltransferase 1 148747363 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Lpcat2 lysophosphatidylcholine acyltransferase 2 27370522 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Lpcat3 lysophospholipid acyltransferase 5 568940713 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Lpcat4 lysophospholipid acyltransferase LPCAT4 46402175 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Lpin1 phosphatidate phosphatase LPIN1 194353985 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Lpin2 phosphatidate phosphatase LPIN2 259089106 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Lpin3 phosphatidate phosphatase LPIN3 312283719 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Lpl lipoprotein lipase precursor 126723006 Lipid Metabolism;
Lrat lecithin retinol acyltransferase 12963753 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Lss lanosterol synthase 1039732220 Lipid Metabolism: Carotenoids and Isoprenoids; Isoprenoids; Lipids; Steroids; Isoprene Metabolism; Products of Isoprene Metabolism;
Lypla1 acyl-protein thioesterase 1 568905274 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids;
Lypla2 acyl-protein thioesterase 2 568931269 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids;
Lyplal1 lysophospholipase-like protein 1 * 755496324
Macrod1 O-acetyl-ADP-ribose deacetylase MACROD1* 170650601
Macrod2 O-acetyl-ADP-ribose deacetylase MACROD2 0* 1039762077
Maoa amine oxidase [flavin-containing] A 255759902 Amino Acid Metabolism: Histidine; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Histidine Metabolism; Porphyrins; Vitamins, Co-Enzymes, and Hormones; Catecholamines;
Maob amine oxidase [flavin-containing] B 257196228 Amino Acid Metabolism: Histidine; Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Histidine Metabolism; Porphyrins; Vitamins, Co-Enzymes, and Hormones; Catecholamines;
Marc1 mitochondrial amidoxime reducing component 2 * 568911764
Marc2 mitochondrial amidoxime-reducing component 1 * 568911768
Mars methionine--tRNA ligase, cytoplasmic 284172357 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Mars2 methionine--tRNA ligase, mitochondrial 30425166 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Mat1a S-adenosylmethionine synthase isoform type-1 19526790 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Carbohydrate Metabolism: Amino Sugar Derivatives; Lipid Metabolism: Fatty Acids; Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Amino Sugars; Ketone Bodies; Purines; Pyrimidine Biosynthesis; Sulfur Metabolism; Amino Acids; Carbohydrates; Amino acids; Lipid degradation; Polysaccharides; Lipid Metabolism; Purine Metabolism; Pyrimidine Metabolism;
Mat2a S-adenosylmethionine synthase isoform type-2 21704144 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Carbohydrate Metabolism: Amino Sugar Derivatives; Lipid Metabolism: Fatty Acids; Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Amino Sugars; Ketone Bodies; Purines; Pyrimidine Biosynthesis; Sulfur Metabolism; Amino Acids; Carbohydrates; Amino acids; Lipid degradation; Polysaccharides; Lipid Metabolism; Purine Metabolism; Pyrimidine Metabolism;
Mat2b methionine adenosyltransferase 2 subunit beta 313482787 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Carbohydrate Metabolism: Amino Sugar Derivatives; Lipid Metabolism: Fatty Acids; Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Amino Sugars; Ketone Bodies; Purines; Pyrimidine Biosynthesis; Sulfur Metabolism; Amino Acids; Carbohydrates; Amino acids; Lipid degradation; Polysaccharides; Lipid Metabolism; Purine Metabolism; Pyrimidine Metabolism;
Mboat1 lysophospholipid acyltransferase 1 755544232 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Mboat2 membrane-bound O-acyltransferase domain-containing protein 2 1039741765 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Mcat malonyl-CoA-acyl carrier protein transacylase, mitochondrial 71725343 Lipid Metabolism: Fatty Acids; Fatty Acid Synthesis; Carbohydrates; Lipid Metabolism;
Mccc1 methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial 186700620 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids; Amino Acids; Amino acids;
Mccc2 methylcrotonoyl-CoA carboxylase beta chain, mitochondrial 73622267 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids; Amino Acids; Amino acids;
Mcee methylmalonyl-CoA epimerase, mitochondrial 568948570 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids; Gluconeogenesis and Glycolysis;
Mdh1 malate dehydrogenase, cytoplasmic 939977622 Citrate and Glyoxalate Cycle; Citrate Cycle; Glyoxylate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Anaplerotic Reactions of the TCA Cycle; Deamination of Amino Acids: The Urea Cycle; Gluconeogenesis and Glycolysis; Glycolysis and TCA Cycle; Lipid Metabolism;
Mdh2 malate dehydrogenase, mitochondrial precursor 31982186 Citrate and Glyoxalate Cycle; Citrate Cycle; Glyoxylate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Anaplerotic Reactions of the TCA Cycle; Deamination of Amino Acids: The Urea Cycle; Gluconeogenesis and Glycolysis; Glycolysis and TCA Cycle; Lipid Metabolism;
Mdp1 magnesium-dependent phosphatase 1 1039746777 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Me1 NADP-dependent malic enzyme 755529755 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Anaplerotic Reactions of the TCA Cycle; Lipid Metabolism;
Me2 NAD-dependent malic enzyme, mitochondrial 221316701 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Anaplerotic Reactions of the TCA Cycle; Lipid Metabolism;
Me3 NADP-dependent malic enzyme, mitochondrial 1039776915 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Anaplerotic Reactions of the TCA Cycle; Lipid Metabolism;
Mecr trans-2-enoyl-CoA reductase, mitochondrial * 755509676
Metap1d methionine aminopeptidase 1D, mitochondrial * 17975502
Mettl1 tRNA (guanine-N(7)-)-methyltransferase* 6754682
Mettl10 protein-lysine N-methyltransferase Mettl10 * 1039780002
Mettl13 methyltransferase-like protein 13 * 568911146
Mettl14 N6-adenosine-methyltransferase subunit METTL14* 260099682
Mettl15 probable methyltransferase-like protein 15 * 755500809
Mettl16 methyltransferase-like protein 16 * 1039737986
Mettl17 methyltransferase-like protein 17, mitochondrial * 71725396
Mettl18 histidine protein methyltransferase 1 homolog * 568911142
Mettl2 methyltransferase-like protein 2 * 568974778
Mettl20 electron transfer flavoprotein beta subunit lysine methyltransferase * 1039775273
Mettl3 N6-adenosine-methyltransferase subunit METTL3* 77627973
Mettl4 methyltransferase-like protein 4 * 1039754760
Mettl5 methyltransferase-like protein 5 * 1039762185
Mettl6 methyltransferase-like protein 6 * 1039746729
Mettl8 methyltransferase-like protein 8 * 161377431
Mettl9 methyltransferase-like protein 9 * 34328259
Mgam maltase-glucoamylase, intestinal 755516655 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Mgll monoglyceride lipase 755516671 Lipid Metabolism;
Mgme1 mitochondrial genome maintenance exonuclease 1 * 568918660
Mgmt methylated-DNA--protein-cysteine methyltransferase 568949763 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids;
Mgst1 microsomal glutathione S-transferase 1 31981068 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Mgst2 microsomal glutathione S-transferase 2 755503585 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Mgst3 microsomal glutathione S-transferase 3 13385010 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Miox inositol oxygenase 45504405 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrates; Hexoses;
Mlycd malonyl-CoA decarboxylase, mitochondrial 1039790410 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Lipid Metabolism: Fatty Acids; Fatty Acid Synthesis; Sulfur Metabolism; Carbohydrates; Glycolysis in the Cytoplasm; Lipid Metabolism;
Mmab cob(I)yrinic acid a,c-diamide adenosyltransferase, mitochondrial * 568937575
Mmachc methylmalonic aciduria and homocystinuria type C protein homolog* 156105691
Mocs1 molybdenum cofactor biosynthesis protein 1 * 569001129
Mocs2 molybdopterin synthase sulfur carrier subunit isoform Mocs2B2* 164664484
Mocs3 adenylyltransferase and sulfurtransferase MOCS3* 237820699
Mogat1 2-acylglycerol O-acyltransferase 1 229577408 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Mogat2 2-acylglycerol O-acyltransferase 2 28974982 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Mogat3 2-acylglycerol O-acyltransferase 3 isoform a 30039700 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Mpi mannose-6-phosphate isomerase 91206392 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Polysaccharides;
Mpst 3-mercaptopyruvate sulfurtransferase 568992501 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Mrm1 rRNA methyltransferase 1, mitochondrial * 89337263
Mrm2 rRNA methyltransferase 2, mitochondrial* 13386002
Msra mitochondrial peptide methionine sulfoxide reductase * 755547652
Msrb1 methionine-R-sulfoxide reductase B1* 7305479
Msrb2 methionine-R-sulfoxide reductase B2, mitochondrial * 1039762252
Msrb3 methionine-R-sulfoxide reductase B3, mitochondrial * 568967806
mt-Co1 cytochrome c oxidase subunit I 116993 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
mt-Co2 cytochrome c oxidase subunit II 117043 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
mt-Co3 cytochrome c oxidase subunit III 117075 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Mthfd1 C-1-tetrahydrofolate synthase, cytoplasmic 261878543 C1-Metabolism; One Carbon Pool; Folic Acid Metabolism;
Mthfd1l monofunctional C1-tetrahydrofolate synthase, mitochondrial 568964682 C1-Metabolism; One Carbon Pool; Folic Acid Metabolism;
Mthfd2 bifunctional methylenetetrahydrofolate dehydrogenase/cyclohydrolase, mitochondrial 755516251 C1-Metabolism; One Carbon Pool; Folic Acid Metabolism;
Mthfd2l bifunctional methylenetetrahydrofolate dehydrogenase/cyclohydrolase 2 568936126 C1-Metabolism; One Carbon Pool; Folic Acid Metabolism;
Mthfr methylenetetrahydrofolate reductase isoform X6 568930739 C1-Metabolism; One Carbon Pool; Folic Acid Metabolism;
Mthfs 5-formyltetrahydrofolate cyclo-ligase 18093092 C1-Metabolism; One Carbon Pool; Folic Acid Metabolism;
mt-Nd1 NADH dehydrogenase subunit 1 (mitochondrion) 128653 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
mt-Nd2 NADH dehydrogenase subunit 2 (mitochondrion) 1352552 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
mt-Nd3 NADH dehydrogenase subunit 3 (mitochondrion) 128726 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
mt-Nd4 NADH dehydrogenase subunit 4 (mitochondrion) 128764 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
mt-Nd4l NADH dehydrogenase subunit 4L (mitochondrion) 128897 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
mt-Nd5 NADH dehydrogenase subunit 5 (mitochondrion) 228015041 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
mt-Nd6 NADH dehydrogenase subunit 6 (mitochondrion) 1352596 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Mto1 protein MTO1 homolog, mitochondrial * 171460946
Mtr methionine synthase 124487479 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids; Folic Acid Metabolism; Folic Acid Reactions;
Mut methylmalonyl-CoA mutase, mitochondrial isoform X2 1039752856 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids; Gluconeogenesis and Glycolysis;
Mutyh adenine DNA glycosylase * 941355860
Mvd diphosphomevalonate decarboxylase 256985114 Lipid Metabolism: Carotenoids and Isoprenoids; Isoprenoids; Lipids; Phospholipids; Isoprene Metabolism; Products of Isoprene Metabolism;
Mvk mevalonate kinase 568936904 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Lipids; Phospholipids; Isoprene Metabolism; Products of Isoprene Metabolism;
Nadk NAD kinase isoform X3 568930825 Nucleotide Metabolism: NAD, NADP;
Nadk2 NAD kinase 2, mitochondrial 555943852 Nucleotide Metabolism: NAD, NADP;
Nadsyn1 glutamine-dependent NAD(+) synthetase 1039780390 Nucleotide Metabolism: NAD, NADP; Vitamins, Co-Enzymes, and Hormones; Aromatic amino acids;
Naglu alpha-N-acetylglucosaminidase 254910995 Carbohydrate Metabolism: Amino Sugar Derivatives; Amino Sugars;
Nags N-acetylglutamate synthase, mitochondrial * 22003874
Nanp N-acylneuraminate-9-phosphatase 568918173 Carbohydrate Metabolism: Amino Sugar Derivatives; Amino Sugars; Carbohydrates; Polysaccharides;
Nans N-acetylneuraminic acid synthase 16716467 Carbohydrate Metabolism: Amino Sugar Derivatives; Amino Sugars; Carbohydrates; Polysaccharides;
Naprt1 nicotinate phosphoribosyltransferase 46485387 Nucleotide Metabolism: NAD, NADP; Vitamins, Co-Enzymes, and Hormones; Aromatic amino acids;
Nars2 probable asparagine--tRNA ligase, mitochondrial * 157951696
Nat1 arylamine N-acetyltransferase 1 755525833 Vitamins, Co-Enzymes, and Hormones; Aromatic amino acids;
Nat2 arylamine N-acetyltransferase 2 568955296 Vitamins, Co-Enzymes, and Hormones; Aromatic amino acids;
Nat3 arylamine N-acetyltransferase 3 isoform X4 6679016 Vitamins, Co-Enzymes, and Hormones; Aromatic amino acids;
Naxd ATP-dependent (S)-NAD(P)H-hydrate dehydratase isoform 3* 652698252
ND1 NADH dehydrogenase subunit 1 (mitochondrion) 1037241539 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
ND2 NADH dehydrogenase subunit 2 (mitochondrion) 1037241540 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
ND3 NADH dehydrogenase subunit 3 (mitochondrion) 1037241546 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
ND4 NADH dehydrogenase subunit 4 (mitochondrion) 1037241548 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
ND4L NADH dehydrogenase subunit 4L (mitochondrion) 1037241547 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
ND5 NADH dehydrogenase subunit 5 (mitochondrion) 1037241549 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
ND6 NADH dehydrogenase subunit 6 (mitochondrion) 1037241550 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndor1 NADPH-dependent diflavin oxidoreductase 1 isoform 3* 357527452
Ndufa1 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1 9506911 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufa10 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 10, mitochondrial precursor 13195624 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufa11 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 11 226437665 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufa12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12 27228985 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufa13 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 13-like 12963633 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufa2 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 2 31981600 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufa3 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 3 21539587 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufa4 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 4 33563266 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufa5 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 5 901694076 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufa6 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 6 13385492 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufa7 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 7 12963571 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufa8 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 8 21312012 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufa9 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 9, mitochondrial 254692859 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufaf1 complex I intermediate-associated protein 30, mitochondrial* 31980802
Ndufaf2 mimitin, mitochondrial * 568984737
Ndufaf3 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3* 12963603
Ndufaf4 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4* 21624617
Ndufaf5 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 * 755500503
Ndufaf6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 * 755506936
Ndufaf7 NADH dehydrogenase [ubiquinone] complex I, assembly factor 7 * 569001778
Ndufaf8 uncharacterized protein C17orf89 homolog* 159106929
Ndufb1 NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 1 38569473 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufb10 NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 10 58037109 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufb11 NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 11, mitochondrial 569008609 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufb2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2 568942710 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufb3 NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 3 13385054 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufb4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex 4 21314826 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufb5 NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 5, mitochondrial 568921009 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufb6 NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 6 84781779 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufb7 NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 7 13385322 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufb8 NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 8, mitochondrial 569007709 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufb9 NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 9 29789148 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufc1 NADH dehydrogenase [ubiquinone] 1 subunit C1, mitochondrial * 13384946
Ndufc2 NADH dehydrogenase [ubiquinone] 1 subunit C2* 18859597
Ndufs1 NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial precursor 568906305 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufs2 NADH dehydrogenase [ubiquinone] iron-sulfur protein 2, mitochondrial precursor 23346461 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufs3 NADH dehydrogenase [ubiquinone] iron-sulfur protein 3, mitochondrial 58037117 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufs4 NADH dehydrogenase [ubiquinone] iron-sulfur protein 4, mitochondrial precursor 281485615 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufs5 NADH dehydrogenase [ubiquinone] iron-sulfur protein 5 72004262 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufs6 NADH dehydrogenase [ubiquinone] iron-sulfur protein 6, mitochondrial precursor 56711244 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufs7 NADH dehydrogenase [ubiquinone] iron-sulfur protein 7, mitochondrial 568968863 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufs8 NADH dehydrogenase [ubiquinone] iron-sulfur protein 8, mitochondrial 406855425 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufv1 NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial 19526814 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufv2 NADH dehydrogenase [ubiquinone] flavoprotein 2, mitochondrial precursor 510025446 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Ndufv3 NADH dehydrogenase [ubiquinone] flavoprotein 3, mitochondrial isoform 1 140969946 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Neu1 sialidase-1 * 254939721
Neu2 sialidase-2 * 568908940
Neu3 sialidase-3* 7710068
Neu4 sialidase-4 * 894216196
Nfs1 cysteine desulfurase, mitochondrial * 568915747
Nit1 nitrilase homolog 1 * 568910903
Nit2 omega-amidase NIT2* 12963555
Nme1 nucleoside diphosphate kinase A 37700232 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Nme2 nucleoside diphosphate kinase B 117606270 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Nme2p1 putative nucleoside diphosphate kinase 3914116 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Nme3 nucleoside diphosphate kinase 3 precursor 255308888 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Nme4 nucleoside diphosphate kinase, mitochondrial 569001119 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Nme5 nucleoside diphosphate kinase homolog 5-like 110625839 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Nme6 nucleoside diphosphate kinase 6 568964012 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Nme7 nucleoside diphosphate kinase 7 568910543 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Nmnat1 nicotinamide mononucleotide adenylyltransferase 1 568931749 Nucleotide Metabolism: NAD, NADP; Vitamins, Co-Enzymes, and Hormones; Aromatic amino acids;
Nmnat2 nicotinamide mononucleotide adenylyltransferase 2 568908798 Nucleotide Metabolism: NAD, NADP; Vitamins, Co-Enzymes, and Hormones; Aromatic amino acids;
Nmnat3 nicotinamide nucleotide adenylyltransferase 3 21362329 Nucleotide Metabolism: NAD, NADP; Vitamins, Co-Enzymes, and Hormones; Aromatic amino acids;
Nnt NAD(P) transhydrogenase, mitochondrial 819023691 Nucleotide Metabolism: NAD, NADP;
Nos1 nitric oxide synthase, brain 1039770698 Amino Acids; Amino acids; Deamination of Amino Acids: The Urea Cycle;
Nos2 nitric oxide synthase, inducible 568972112 Amino Acids; Amino acids; Deamination of Amino Acids: The Urea Cycle;
Nos3 nitric oxide synthase, endothelial 568933039 Amino Acids; Amino acids; Deamination of Amino Acids: The Urea Cycle;
Npl N-acetylneuraminate lyase 21311855 Carbohydrate Metabolism: Amino Sugar Derivatives; Amino Sugars;
Nrd1 nardilysin * 1039767400
Nsun2 tRNA (cytosine(34)-C(5))-methyltransferase* 295054316
Nsun3 putative methyltransferase NSUN3 * 755553034
Nsun4 putative methyltransferase NSUN4* 21312358
Nsun5 probable 28S rRNA (cytosine-C(5))-methyltransferase* 154146245
Nsun6 putative methyltransferase NSUN6 isoform c* 260099664
Nsun7 putative methyltransferase NSUN7 * 725503325
Nt5c 5'(3')-deoxyribonucleotidase, cytosolic type * 755539074
Nt5c1a cytosolic 5'-nucleotidase 1A 148227160 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Nt5c1b cytosolic 5'-nucleotidase 1B 568978008 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Nt5c2 cytosolic purine 5'-nucleotidase isoform 3 1039758323 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Nt5c3a cytosolic 5'-nucleotidase 3A 157823103 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Nt5c3b 7-methylguanosine phosphate-specific 5'-nucleotidase 156627553 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Nt5dc1 5'-nucleotidase domain-containing protein 1 110626010 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Nt5dc2 5'-nucleotidase domain-containing protein 2 568988697 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Nt5dc3 5'-nucleotidase domain-containing protein 3 isoform X2 111494223 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Nt5dc4 5'-nucleotidase domain-containing protein 4 530357747 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Nt5e 5'-nucleotidase precursor 6754900 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Fatty Acid Oxidation; Phosphatides; Purines; Pyrimidine Biosynthesis; Pyrimidines; Lipids; Purines and Pyrimidines; Phospholipids; Purines; Purine Metabolism;
Nt5m 5'(3')-deoxyribonucleotidase, mitochondrial 20127399 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Nthl1 endonuclease III-like protein 1 * 568999351
Ntpcr nucleoside-triphosphatase C1orf57 homolog 755527154 Pyrimidine Metabolism;
Nudt1 7,8-dihydro-8-oxoguanine triphosphatase * 6678950
Nudt10 diphosphoinositol polyphosphate phosphohydrolase 3-alpha* 72384357
Nudt11 diphosphoinositol polyphosphate phosphohydrolase 3-beta* 72384359
Nudt12 peroxisomal NADH pyrophosphatase NUDT12 * 569001443
Nudt13 nucleoside diphosphate-linked moiety X motif 13 * 1039746760
Nudt14 uridine diphosphate glucose pyrophosphatase * 941355814
Nudt15 probable 8-oxo-dGTP diphosphatase NUDT15* 27369730
Nudt16 U8 snoRNA-decapping enzyme * 568963196
Nudt17 nucleoside diphosphate-linked moiety X motif 17 * 242397442
Nudt18 8-oxo-dGDP phosphatase NUDT18 * 568987213
Nudt19 nucleoside diphosphate-linked moiety X motif 19 * 94158950
Nudt2 bis(5'-nucleosyl)-tetraphosphatase [asymmetrical] * 755506697
Nudt3 diphosphoinositol polyphosphate phosphohydrolase 1 * 597517975
Nudt4 diphosphoinositol polyphosphate phosphohydrolase 2 * 568968542
Nudt5 ADP-sugar pyrophosphatase* 8393853
Nudt6 nucleoside diphosphate-linked moiety X motif 6 * 1039764166
Nudt7 peroxisomal coenzyme A diphosphatase NUDT7 * 1039790598
Nudt8 nucleoside diphosphate-linked moiety X motif 8* 13384950
Nudt9 ADP-ribose pyrophosphatase, mitochondrial * 568936289
Oat ornithine aminotransferase, mitochondrial precursor 8393866 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids;
Obscn obscurin * 345842337
Odc1 ornithine decarboxylase 1039739932 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids;
Ogdh 2-oxoglutarate dehydrogenase, mitochondrial precursor 1039736048 Amino Acid Metabolism: Lysine; Citrate and Glyoxalate Cycle; Glyoxylate Cycle; Lysine Metabolism; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle;
Ogdhl 2-oxoglutarate dehydrogenase-like, mitochondrial 568987554 Amino Acid Metabolism: Lysine; Citrate and Glyoxalate Cycle; Glyoxylate Cycle; Lysine Metabolism; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle;
Ogg1 N-glycosylase/DNA lyase* 187960092
Olah S-acyl fatty acid synthase thioesterase, medium chain 22122331 Citrate and Glyoxalate Cycle; Lipid Metabolism: Fatty Acids; Citrate Cycle; Fatty Acid Synthesis; Glyoxylate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Anaplerotic Reactions of the TCA Cycle; Deamination of Amino Acids: The Urea Cycle; Gluconeogenesis and Glycolysis; Glycolysis and TCA Cycle; Lipid Metabolism;
Ostc oligosaccharyltransferase complex subunit OSTC 13384930 Lipid Metabolism: Fatty Acids; Lipid Metabolism;
Otc ornithine carbamoyltransferase, mitochondrial precursor 755564474 Amino Acid Metabolism: Urea Cycle; Urea Cycle; Amino Acids; Amino acids; Deamination of Amino Acids: The Urea Cycle;
Oxct1 succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial precursor 18266680 Lipid Metabolism: Fatty Acids; Ketone Bodies;
Oxct2 succinyl-CoA:3-ketoacid coenzyme A transferase 2, mitochondrial precursor 11545841 Lipid Metabolism: Fatty Acids; Ketone Bodies;
Oxct2a succinyl-CoA:3-ketoacid coenzyme A transferase 2A, mitochondrial precursor 11968160 Lipid Metabolism: Fatty Acids; Ketone Bodies;
Oxct2b succinyl-CoA:3-ketoacid coenzyme A transferase 2B, mitochondrial precursor 160358827 Lipid Metabolism: Fatty Acids; Ketone Bodies;
Oxnad1 oxidoreductase NAD-binding domain-containing protein 1 * 1039745954
Oxsm 3-oxoacyl-[acyl-carrier-protein] synthase, mitochondrial 568985611 Lipid Metabolism: Fatty Acids; Fatty Acid Synthesis; Carbohydrates; Lipid biosynthesis;
P4ha1 prolyl 4-hydroxylase subunit alpha-1 precursor 568966918 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids;
P4ha2 prolyl 4-hydroxylase subunit alpha-2 precursor 568972124 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids;
P4ha3 prolyl 4-hydroxylase subunit alpha-3 precursor 755522787 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids;
P4hb protein disulfide-isomerase * 42415475
Pah phenylalanine-4-hydroxylase 171543886 Amino Acid Metabolism: Histidine; Histidine Metabolism; Amino Acids; Aromatic amino acids;
Paics phosphoribosylaminoimidazole-succinocarboxamide synthase 1039772373 Nucleotide Metabolism: Purines; Purine Biosynthesis; Purines and Pyrimidines; Purines; Purine Metabolism;
Pank1 pantothenate kinase 1 569007999 Cofactors and Vitamins: Coenzyme A; Vitamins, Co-Enzymes, and Hormones; Amino acids;
Pank2 pantothenate kinase 2 (Hallervorden-Spatz syndrome) 1039762155 Cofactors and Vitamins: Coenzyme A; Vitamins, Co-Enzymes, and Hormones; Amino acids;
Pank3 pantothenate kinase 3 22122397 Cofactors and Vitamins: Coenzyme A; Vitamins, Co-Enzymes, and Hormones; Amino acids;
Pank4 pantothenate kinase 4 1039767892 Cofactors and Vitamins: Coenzyme A; Vitamins, Co-Enzymes, and Hormones; Amino acids;
Papd4 poly(A) RNA polymerase GLD2 1039742921 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Papd5 non-canonical poly(A) RNA polymerase PAPD5 1039788226 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Papd7 DNA polymerase sigma 568983222 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Papss1 bifunctional 3'-phosphoadenosine 5'-phosphosulfate synthase 1 575403001 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids;
Papss2 bifunctional 3'-phosphoadenosine 5'-phosphosulfate synthase 2 569007205 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids;
Park2 E3 ubiquitin-protein ligase parkin * 1039753958
Park7 protein DJ-1* 55741460
Pars2 probable proline--tRNA ligase, mitochondrial * 568928790
Pc pyruvate carboxylase, mitochondrial precursor 31543464 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Anaplerotic Reactions of the TCA Cycle; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation; Lipid Metabolism;
Pcbd1 pterin-4-alpha-carbinolamine dehydratase* 13384608
Pcbd2 pterin-4-alpha-carbinolamine dehydratase 2 * 755545621
Pcca propionyl-CoA carboxylase alpha chain, mitochondrial 755547658 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids; Gluconeogenesis and Glycolysis;
Pccb propionyl-CoA carboxylase beta chain, mitochondrial precursor 568961907 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism; Amino Acids; Amino acids; Gluconeogenesis and Glycolysis;
Pck1 phosphoenolpyruvate carboxykinase, cytosolic [GTP] 7110683 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Anaplerotic Reactions of the TCA Cycle; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation;
Pck2 phosphoenolpyruvate carboxykinase 2 (mitochondrial) 28077029 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Anaplerotic Reactions of the TCA Cycle; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation;
Pcx pyruvate carboxylase, mitochondrial * 569005643
Pcyt1a choline-phosphate cytidylyltransferase A 253683458 Lipid Metabolism: Glyco- and Phospholipids; Lipids; Phospholipids;
Pcyt1b choline-phosphate cytidylyltransferase B 569010043 Lipid Metabolism: Glyco- and Phospholipids; Lipids; Phospholipids;
Pcyt2 ethanolamine-phosphate cytidylyltransferase 568975514 Lipid Metabolism: Glyco- and Phospholipids; Lipids; Phospholipids;
Pde10a cAMP and cAMP-inhibited cGMP 3',5'-cyclic phosphodiesterase 10A 1039753500 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde11a dual 3',5'-cyclic-AMP and -GMP phosphodiesterase 11A isoform 2 568916897 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde12 2',5'-phosphodiesterase 12 40538842 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde1a calcium/calmodulin-dependent 3',5'-cyclic nucleotide phosphodiesterase 1A 755498910 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde1b calcium/calmodulin-dependent 3',5'-cyclic nucleotide phosphodiesterase 1B 1039748435 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde1c calcium/calmodulin-dependent 3',5'-cyclic nucleotide phosphodiesterase 1C 1039774523 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde2a cGMP-dependent 3',5'-cyclic phosphodiesterase isoform PDE2A1 1039777758 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde3a cGMP-inhibited 3',5'-cyclic phosphodiesterase A 755518671 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde3b cGMP-inhibited 3',5'-cyclic phosphodiesterase B 568949823 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde4a cAMP-specific 3',5'-cyclic phosphodiesterase 4A 1039792332 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde4b cAMP-specific 3',5'-cyclic phosphodiesterase 4B 1039766903 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde4c cAMP-specific 3',5'-cyclic phosphodiesterase 4C 755525776 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde4d cAMP-specific 3',5'-cyclic phosphodiesterase 4D isoform 4 568984467 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde5a cGMP-specific 3',5'-cyclic phosphodiesterase 568922793 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde6a rod cGMP-specific 3',5'-cyclic phosphodiesterase subunit alpha 569003748 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde6b rod cGMP-specific 3',5'-cyclic phosphodiesterase subunit beta 113930735 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde6c cone cGMP-specific 3',5'-cyclic phosphodiesterase subunit alpha' 284005078 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde6d retinal rod rhodopsin-sensitive cGMP 3',5'-cyclic phosphodiesterase subunit delta 755493918 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde7a high affinity cAMP-specific 3',5'-cyclic phosphodiesterase 7A 755502633 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde7b cAMP-specific 3',5'-cyclic phosphodiesterase 7B 568965449 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde8a high affinity cAMP-specific and IBMX-insensitive 3',5'-cyclic phosphodiesterase 8A 6679249 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde8b high affinity cAMP-specific and IBMX-insensitive 3',5'-cyclic phosphodiesterase 8B 1039743625 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pde9a high affinity cGMP-specific 3',5'-cyclic phosphodiesterase 9A 1039752924 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides;
Pdha1 pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial precursor 6679261 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Branched Chain Amino Acids; Carbohydrates; Glycolysis in the Cytoplasm; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle; Lipid Metabolism;
Pdha2 pyruvate dehydrogenase E1 component subunit alpha, testis-specific form, mitochondrial precursor 6679263 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Branched Chain Amino Acids; Carbohydrates; Glycolysis in the Cytoplasm; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle; Lipid Metabolism;
Pdhb pyruvate dehydrogenase E1 component subunit beta, mitochondrial precursor 18152793 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Branched Chain Amino Acids; Carbohydrates; Glycolysis in the Cytoplasm; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle; Lipid Metabolism;
Pdhx pyruvate dehydrogenase protein X component, mitochondrial* 28201978
Pdk1 pyruvate dehydrogenase kinase, isozyme 1 precursor 110625975 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions;
Pdk2 pyruvate dehydrogenase kinase, isozyme 2 568972134 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions;
Pdk3 pyruvate dehydrogenase kinase, isozyme 3 21704122 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions;
Pdk4 pyruvate dehydrogenase kinase, isozyme 4 7305375 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions;
Pdp1 [Pyruvate dehydrogenase [acetyl-transferring]]-phosphatase 1, mitochondrial isoform 1 594190788 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Pdp2 [Pyruvate dehydrogenase [acetyl-transferring]]-phosphatase 2, mitochondrial precursor 568957129 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Carbohydrates; TCA Cycle in the Mitochondrial Matrix;
Pdpr pyruvate dehydrogenase phosphatase regulatory subunit, mitochondrial 1039790120 Lipid Metabolism: Glyco- and Phospholipids; Amino Acids; Amino acids;
Pdss1 decaprenyl-diphosphate synthase subunit 1 1039761403 Lipid Metabolism: Carotenoids and Isoprenoids; Isoprenoids;
Pdss2 decaprenyl-diphosphate synthase subunit 2 568965648 Lipid Metabolism: Carotenoids and Isoprenoids; Isoprenoids;
Pdxp pyridoxal phosphate phosphatase 47059486 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Amino Acids; Amino acids;
Pemt phosphatidylethanolamine N-methyltransferase 586597942 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Lipids; Phospholipids;
Peo1 twinkle protein, mitochondrial * 569007079
Pfas phosphoribosylformylglycinamidine synthase 226958458 Nucleotide Metabolism: Purines; Purine Biosynthesis; Purines and Pyrimidines; Purines; Purine Metabolism;
Pfkfb1 6-phosphofructo-2-kinase/fructose-2,6-bisphosphatase 1 isoform 3 755566430 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Glycolysis;
Pfkfb2 6-phosphofructo-2-kinase/fructose-2,6-bisphosphatase 2 isoform c 241666430 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Glycolysis;
Pfkfb3 6-phosphofructo-2-kinase/fructose-2,6-bisphosphatase 3 1039759256 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Glycolysis;
Pfkfb4 6-phosphofructo-2-kinase/fructose-2,6-bisphosphatase 4 1039793391 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Glycolysis;
Pfkl ATP-dependent 6-phosphofructokinase, liver type 1039732434 Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation; Glycolysis and TCA Cycle; Pentose Phosphate Pathways;
Pfkm ATP-dependent 6-phosphofructokinase, muscle type 254553348 Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation; Glycolysis and TCA Cycle; Pentose Phosphate Pathways;
Pfkp ATP-dependent 6-phosphofructokinase, platelet type 568981400 Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation; Glycolysis and TCA Cycle; Pentose Phosphate Pathways;
Pgam1 phosphoglycerate mutase 1 114326546 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis;
Pgam2 phosphoglycerate mutase 2 9256624 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis;
Pgam4 phosphoglycerate mutase 4 71274132 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis;
Pgam5 serine/threonine-protein phosphatase PGAM5, mitochondrial 254587962 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis;
Pgd 6-phosphogluconate dehydrogenase, decarboxylating 1039766370 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Glycolysis; Carbohydrates; Pentose Phosphate Pathways;
Pgk1 phosphoglycerate kinase 1 70778976 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Glycolysis and TCA Cycle;
Pgk2 phosphoglycerate kinase 2 226246531 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Glycolysis and TCA Cycle;
Pgls 6-phosphogluconolactonase 659928105 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Isoprene Metabolism;
Pgm1 phosphoglucomutase-1 33859686 Carbohydrate Metabolism: Amino Sugar Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Polysaccharides;
Pgm2 phosphoglucomutase-2 227330633 Carbohydrate Metabolism: Amino Sugar Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Polysaccharides;
Pgm3 phosphoacetylglucosamine mutase 255522941 Carbohydrate Metabolism: Amino Sugar Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Polysaccharides;
Pgs1 CDP-diacylglycerol--glycerol-3-phosphate 3-phosphatidyltransferase, mitochondrial isoform X3 110626163 Lipid Metabolism: Glyco- and Phospholipids; Carbohydrates; Lipid biosynthesis; Phospholipids;
Phgdh D-3-phosphoglycerate dehydrogenase 52353955 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Glycolysis; Amino Acids; Carbohydrates; Amino acids; Glycolysis in the Cytoplasm; Pentose Phosphate Pathways;
Phka1 phosphorylase b kinase regulatory subunit alpha, skeletal muscle isoform 1039796630 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Carbohydrates; Polysaccharides;
Phka2 phosphorylase b kinase regulatory subunit alpha, liver isoform 755566353 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Carbohydrates; Polysaccharides;
Phkb phosphorylase b kinase regulatory subunit beta 1039781374 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Carbohydrates; Polysaccharides;
Phkg1 phosphorylase b kinase gamma catalytic chain, skeletal muscle/heart isoform 755514315 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Carbohydrates; Polysaccharides;
Phkg2 phosphorylase b kinase gamma catalytic chain, liver/testis isoform 1039779839 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Carbohydrates; Polysaccharides;
Phyh phytanoyl-CoA dioxygenase, peroxisomal * 6754564
Pigz GPI mannosyltransferase 4 568995315 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Hexoses; Pentose Phosphate Pathways;
Pisd phosphatidylserine decarboxylase proenzyme isoform X5 1039771790 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Lipids; Phospholipids;
Pklr pyruvate kinase PKLR 568922076 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Carbohydrates; Glycolysis in the Cytoplasm; Anaplerotic Reactions of the TCA Cycle; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation; Glycolysis and TCA Cycle;
Pkm pyruvate kinase PKM 755529787 Carbohydrate Metabolism: Pyruvate Turnover; Anaplerotic Reactions; Carbohydrates; Glycolysis in the Cytoplasm; Anaplerotic Reactions of the TCA Cycle; Gluconeogenesis and Glycolysis; Gluconeogenesis and Glycolysis: Regulation; Glycolysis and TCA Cycle;
Pla2g10 group 10 secretory phospholipase A2 precursor 597436928 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g12a group XIIA secretory phospholipase A2 isoform X2 559098495 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g12b phospholipase A2, group XIIB isoform X1 568968430 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g15 group XV phospholipase A2 precursor 568956338 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g16 group XVI phospholipase A1/A2 84781797 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g1b phospholipase A2 precursor 568936932 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g2a phospholipase A2, membrane associated precursor 132626633 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g2c group IIC secretory phospholipase A2 225543511 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g2d group IID secretory phospholipase A2 precursor 568930809 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g2e group IIE secretory phospholipase A2 568931418 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g2f group IIF secretory phospholipase A2 38454186 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g3 group 3 secretory phospholipase A2 precursor 1039737042 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g4a cytosolic phospholipase A2 779176837 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g4b cytosolic phospholipase A2 beta 167900427 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g4c phospholipase A2, group IVC 1039778142 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g4d cytosolic phospholipase A2 delta-like 67906183 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g4e cytosolic phospholipase A2 epsilon isoform X5 63999319 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g4f cytosolic phospholipase A2 zeta-like isoform X2 67972423 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g5 calcium-dependent phospholipase A2 precursor 1039766948 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g6 85/88 kDa calcium-independent phospholipase A2 isoform 2 1039749224 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pla2g7 platelet-activating factor acetylhydrolase precursor 569000483 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Plb1 phospholipase B1, membrane-associated precursor 568934419 Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Fatty Acid Oxidation; Phosphatides; Lipids; Phospholipids; Prostaglandins, Thromboxanes, and Leucotrienes;
Pld1 phospholipase D1 1039763921 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Lipids; Phospholipids;
Pld2 phospholipase D2 1039736062 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Lipids; Phospholipids;
Pld3 phospholipase D3 1039777590 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Lipids; Phospholipids;
Pld4 phospholipase D4 1039739586 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Lipids; Phospholipids;
Pld5 inactive phospholipase D5 1039729235 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Lipids; Phospholipids;
Pld6 mitochondrial cardiolipin hydrolase-like isoform X1 590114095 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Lipids; Phospholipids;
Plod1 procollagen-lysine,2-oxoglutarate 5-dioxygenase 1 precursor 6755106 Amino Acid Metabolism: Lysine; Lysine Metabolism;
Plod2 procollagen-lysine,2-oxoglutarate 5-dioxygenase 2 isoform 2 precursor 218931167 Amino Acid Metabolism: Lysine; Lysine Metabolism;
Plod3 procollagen-lysine,2-oxoglutarate 5-dioxygenase 3 precursor 6755110 Amino Acid Metabolism: Lysine; Lysine Metabolism;
Pmm1 phosphomannomutase 1 530677962 Carbohydrates; Polysaccharides;
Pmm2 phosphomannomutase 2 568995808 Carbohydrates; Polysaccharides;
Pmvk phosphomevalonate kinase 890825063 Lipid Metabolism: Carotenoids and Isoprenoids; Isoprenoids; Lipids; Phospholipids; Isoprene Metabolism; Products of Isoprene Metabolism;
Pnlip pancreatic triacylglycerol lipase precursor 37674236 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Pnliprp1 inactive pancreatic lipase-related protein 1 precursor 9256628 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Pnliprp2 pancreatic lipase-related protein 2 precursor 160333869 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Pnliprp3 pancreatic lipase-related protein 3 precursor 190341077 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Pnmt phenylethanolamine N-methyltransferase 6679405 Amino Acid Metabolism: Histidine; Lipid Metabolism: Glyco- and Phospholipids; Histidine Metabolism; Phosphatides; Lipids; Vitamins, Co-Enzymes, and Hormones; Catecholamines; Phospholipids;
Pnp purine nucleoside phosphorylase 7305395 Nucleotide Metabolism: Purines; Purines; Purines and Pyrimidines; Purines; Purine Metabolism;
Pnpla1 patatin-like phospholipase domain-containing protein 1 569000927 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Pnpla2 patatin-like phospholipase domain-containing protein 2 254826782 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Pnpla3 patatin-like phospholipase domain containing 3 568991162 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Pnpla4 patatin-like phospholipase domain-containing protein 4 isoform 1 precursor 42415471 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Pnpla5 patatin-like phospholipase domain-containing protein 5 568993591 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Pnpla6 neuropathy target esterase 390608665 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Carotenoids; Fatty Acid Oxidation; Phosphatides; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Phospholipids; Lipid Metabolism; Products of Isoprene Metabolism;
Pnpla7 patatin-like phospholipase domain-containing protein 7 1039760530 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Carotenoids; Fatty Acid Oxidation; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Lipid Metabolism; Products of Isoprene Metabolism;
Pnpla8 calcium-independent phospholipase A2-gamma 118130807 Lipid Metabolism: Carotenoids and Isoprenoids; Lipid Metabolism: Fatty Acids; Lipid Metabolism: Glyco- and Phospholipids; Carotenoids; Fatty Acid Oxidation; Phosphatides; Lipids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Lipid biosynthesis; Phospholipids; Lipid Metabolism; Products of Isoprene Metabolism;
Pnpo pyridoxine-5'-phosphate oxidase* 19527238
Pnpt1 polyribonucleotide nucleotidyltransferase 1, mitochondrial 755536547 Nucleotide Metabolism: Purines;
Pola1 DNA polymerase alpha catalytic subunit 569009877 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Pola2 DNA polymerase alpha subunit B 755562344 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Polb DNA polymerase beta 755524897 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Pold1 DNA polymerase delta catalytic subunit 254587977 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Pold2 DNA polymerase delta subunit 2 568970019 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Pold3 DNA polymerase delta subunit 3 29789321 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Pold4 DNA polymerase delta subunit 4 21312396 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Pole DNA polymerase epsilon catalytic subunit A 1039770739 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Pole2 polymerase (DNA directed), epsilon 2 33468927 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Pole3 DNA polymerase epsilon subunit 3 31981174 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Pole4 DNA polymerase epsilon subunit 4 755517172 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Polg DNA polymerase subunit gamma-1 87080815 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Polg2 DNA polymerase subunit gamma-2, mitochondrial 568974699 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Polh DNA polymerase eta 569002165 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Poli DNA polymerase iota 1039756022 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Polk DNA polymerase kappa 568984531 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Poll DNA polymerase lambda 1059842867 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Polm DNA polymerase mu 568970377 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Poln DNA polymerase nu isoform 3 577019535 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Polq DNA polymerase theta 755554227 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Polr1a DNA-directed RNA polymerase I subunit RPA1 568941206 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr1b DNA-directed RNA polymerase I subunit RPA2 568916007 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr1c DNA-directed RNA polymerases I and III subunit RPAC1 119226251 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr1d DNA-directed RNA polymerases I and III subunit RPAC2 isoform 2 32189421 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr1e DNA-directed RNA polymerase I subunit RPA49 551411429 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr2a DNA-directed RNA polymerase II subunit RPB1 isoform 1 597517934 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr2b DNA-directed RNA polymerase II subunit RPB2 226958589 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr2c DNA-directed RNA polymerase II subunit RPB3 29336059 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr2d DNA-directed RNA polymerase II subunit RPB4 1039756415 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr2e DNA-directed RNA polymerases I, II, and III subunit RPABC1 124249077 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr2f DNA-directed RNA polymerases I, II, and III subunit RPABC2 58037181 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr2g DNA-directed RNA polymerase II subunit RPB7 13385826 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr2h polymerase (RNA) II (DNA directed) polypeptide H 568995350 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr2i DNA-directed RNA polymerase II subunit RPB9 110625757 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr2j polymerase (RNA) II (DNA directed) polypeptide J 188219604 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr2k polymerase (RNA) II (DNA directed) polypeptide K 86355514 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr2l polymerase (RNA) II (DNA directed) polypeptide L 219881031 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr2m DNA-directed RNA polymerase II subunit GRINL1A 258645114 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr3a DNA-directed RNA polymerase III subunit RPC1 568987269 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr3b DNA-directed RNA polymerase III subunit RPC2 46195739 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr3c DNA-directed RNA polymerase III subunit RPC3 568924284 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr3d DNA-directed RNA polymerase III subunit RPC4 568988555 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr3e DNA-directed RNA polymerase III subunit RPC5 1039778830 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr3f DNA-directed RNA polymerase III subunit RPC6 27754160 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr3g DNA-directed RNA polymerase III subunit RPC7 124487177 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polr3h DNA-directed RNA polymerase III subunit RPC8 568993641 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Polrmt DNA-directed RNA polymerase, mitochondrial 281332113 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Ppa1 inorganic pyrophosphatase 27754065 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Ppa2 inorganic pyrophosphatase 2, mitochondrial 568924345 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Ppap2a lipid phosphate phosphohydrolase 1 61889081 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Ppap2b lipid phosphate phosphohydrolase 3 48675867 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Ppap2c lipid phosphate phosphohydrolase 2 21245102 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Ppapdc1a phosphatidate phosphatase PPAPDC1A 300798497 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Ppapdc1b phosphatidate phosphatase PPAPDC1B 198442855 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Ppat amidophosphoribosyltransferase precursor 26024309 Carbohydrate Metabolism: Pentoses and Pentose Cycle; Pentose Cycle; Carbohydrates; Glycolysis in the Cytoplasm; Purine Metabolism;
Ppcdc phosphopantothenoylcysteine decarboxylase 1039793904 Cofactors and Vitamins: Coenzyme A; Vitamins, Co-Enzymes, and Hormones; Amino acids;
Ppcs phosphopantothenate--cysteine ligase 1039766328 Cofactors and Vitamins: Coenzyme A; Vitamins, Co-Enzymes, and Hormones; Amino acids;
Ppif peptidyl-prolyl cis-trans isomerase F, mitochondrial * 1039745247
Ppox protoporphyrinogen oxidase 755495529 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Vitamins, Co-Enzymes, and Hormones; Porphyrins; Heme Metabolism;
Prdx1 peroxiredoxin-1* 6754976
Prdx2 peroxiredoxin-2* 959092670
Prdx3 thioredoxin-dependent peroxide reductase, mitochondrial * 6680690
Prdx4 peroxiredoxin-4 * 922959873
Prdx5 peroxiredoxin-5, mitochondrial * 6755114
Prdx6 peroxiredoxin-6 * 742068536
Prg1 lipid phosphate phosphatase-related protein type 4 325197225 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Prg2 lipid phosphate phosphatase-related protein type 3 6679457 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Prg3 lipid phosphate phosphatase-related protein type 1 568917816 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Prg4 lipid phosphate phosphatase-related protein type 2 1039730453 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis; Lipid Metabolism;
Prim1 primase, DNA, polypeptide 1 6679459 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Prim2 DNA primase large subunit 755492205 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Prkaa1 5'-AMP-activated protein kinase catalytic subunit alpha-1 94681061 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids;
Prkaa2 5'-AMP-activated protein kinase catalytic subunit alpha-2 227452236 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids;
Prodh proline dehydrogenase, mitochondrial isoform X3 568994772 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids;
Prodh2 proline dehydrogenase 2 18139551 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids;
Prps1 ribose-phosphate pyrophosphokinase 1 10946854 Carbohydrate Metabolism: Pentoses and Pentose Cycle; Nucleotide Metabolism: Pyrimidines; Pentose Interconversions; Pyrimidine Biosynthesis; Carbohydrates; Purine Metabolism;
Prps1l1 phosphoribosyl pyrophosphate synthetase 1-like 1 30794182 Carbohydrate Metabolism: Pentoses and Pentose Cycle; Nucleotide Metabolism: Pyrimidines; Pentose Interconversions; Pyrimidine Biosynthesis; Carbohydrates; Purine Metabolism;
Prps2 ribose-phosphate pyrophosphokinase 2 1039796032 Carbohydrate Metabolism: Pentoses and Pentose Cycle; Nucleotide Metabolism: Pyrimidines; Pentose Interconversions; Pyrimidine Biosynthesis; Carbohydrates; Purine Metabolism;
Prtfdc1 phosphoribosyltransferase domain-containing protein 1 157817282 Nucleotide Metabolism: Purines; Purine Metabolism;
Prune protein prune homolog 27597069 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Psat1 phosphoserine aminotransferase 329299029 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Amino Acids; Amino acids;
Psph phosphoserine phosphatase 1039770066 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Amino Acids; Amino acids;
Pstk L-seryl-tRNA(Sec) kinase * 568950066
Ptgds prostaglandin-H2 D-isomerase precursor 119226208 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Ptges prostaglandin E synthase 11967941 Lipids; Lipid biosynthesis; Prostaglandins, Thromboxanes, and Leucotrienes;
Ptges1 prostaglandin E synthase Lipids; Lipid biosynthesis; Prostaglandins, Thromboxanes, and Leucotrienes;
Ptges2 prostaglandin E synthase 2 260763900 Lipids; Lipid biosynthesis; Prostaglandins, Thromboxanes, and Leucotrienes;
Ptges3 prostaglandin E synthase 3 9790017 Lipids; Lipid biosynthesis; Prostaglandins, Thromboxanes, and Leucotrienes;
Ptges3l1 prostaglandin E synthase 3 62079275 Lipids; Lipid biosynthesis; Prostaglandins, Thromboxanes, and Leucotrienes;
Ptgis prostacyclin synthase precursor 6679535 Prostaglandins, Thromboxanes, and Leucotrienes;
Ptgs1 prostaglandin G/H synthase 1 precursor 6679537 Lipids; Lipid biosynthesis;
Ptgs2 prostaglandin G/H synthase 2 precursor 31981525 Lipids; Lipid biosynthesis;
Pts 6-pyruvoyl tetrahydrobiopterin synthase precursor 7110709 Antibiotics: Penicillin, Cephalosporin; Pterine Biosynthesis;
Pus1 tRNA pseudouridine synthase A, mitochondrial * 1039772115
Pus10 putative tRNA pseudouridine synthase Pus10* 75905504
Pus3 tRNA pseudouridine(38/39) synthase * 755529078
Pus7 pseudouridylate synthase 7 homolog * 755511095
Pusl1 tRNA pseudouridine synthase-like 1 * 1039768166
Pycr1 pyrroline-5-carboxylate reductase 1, mitochondrial 21450149 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids;
Pycr2 pyrroline-5-carboxylate reductase 2 19526878 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids;
Pycrl pyrroline-5-carboxylate reductase 3 568993033 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway; Amino Acids; Amino acids;
Pygb glycogen phosphorylase, brain form 24418919 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Carbohydrates; Polysaccharides;
Pygl glycogen phosphorylase, liver form 268836255 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Carbohydrates; Polysaccharides;
Pygm glycogen phosphorylase, muscle form 6755256 Carbohydrate Metabolism: Di-and Polysaccharides; Polysaccharides; Carbohydrates; Polysaccharides;
Qars glutaminyl-tRNA synthetase 269954677 Amino Acid Metabolism: Glutamate, Proline, Hydroxyproline; Mesaconate Pathway;
Qdpr dihydropteridine reductase 21312520 Antibiotics: Penicillin, Cephalosporin; Pterine Biosynthesis;
Qprt nicotinate-nucleotide pyrophosphorylase [carboxylating] 19526852 Nucleotide Metabolism: NAD, NADP; Vitamins, Co-Enzymes, and Hormones; Aromatic amino acids;
Qrsl1 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial* 124486688
Qtrt1 queuine tRNA-ribosyltransferase * 755529056
Rars arginine--tRNA ligase, cytoplasmic 262118273 Amino Acid Metabolism: Urea Cycle; Urea Cycle;
Rars2 arginyl-tRNA synthetase, mitochondrial 1039766351 Amino Acid Metabolism: Urea Cycle; Urea Cycle;
Rbks ribokinase 1039772538 Carbohydrate Metabolism: Pentoses and Pentose Cycle; Pentose Cycle; Carbohydrates; Pentoses;
Rdh1 retinol dehydrogenase 1 (all trans) precursor 568966264 Lipid Metabolism: Carotenoids and Isoprenoids; Steroid Metabolism: Androgens and Estrogens; Carotenoids; Estrogens; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Rdh10 retinol dehydrogenase 10 25141231 Lipid Metabolism: Carotenoids and Isoprenoids; Steroid Metabolism: Androgens and Estrogens; Carotenoids; Estrogens; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Rdh11 retinol dehydrogenase 11 precursor 19482172 Lipid Metabolism: Carotenoids and Isoprenoids; Steroid Metabolism: Androgens and Estrogens; Carotenoids; Estrogens; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Rdh12 retinol dehydrogenase 12 precursor 927928789 Lipid Metabolism: Carotenoids and Isoprenoids; Steroid Metabolism: Androgens and Estrogens; Carotenoids; Estrogens; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Rdh13 retinol dehydrogenase 13 precursor 755518998 Lipid Metabolism: Carotenoids and Isoprenoids; Steroid Metabolism: Androgens and Estrogens; Carotenoids; Estrogens; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Rdh14 retinol dehydrogenase 14 12963791 Lipid Metabolism: Carotenoids and Isoprenoids; Steroid Metabolism: Androgens and Estrogens; Carotenoids; Estrogens; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Rdh16 retinol dehydrogenase 2 precursor 568967027 Lipid Metabolism: Carotenoids and Isoprenoids; Steroid Metabolism: Androgens and Estrogens; Carotenoids; Estrogens; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Rdh19 retinol dehydrogenase similar protein 2 precursor 117320520 Lipid Metabolism: Carotenoids and Isoprenoids; Steroid Metabolism: Androgens and Estrogens; Carotenoids; Estrogens; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Rdh2 retinol dehydrogenase 2 precursor 40363270 Lipid Metabolism: Carotenoids and Isoprenoids; Steroid Metabolism: Androgens and Estrogens; Carotenoids; Estrogens; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Rdh5 11-cis retinol dehydrogenase 19549323 Lipid Metabolism: Carotenoids and Isoprenoids; Steroid Metabolism: Androgens and Estrogens; Carotenoids; Estrogens; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Rdh7 retinol dehydrogenase 7 precursor 226510365 Lipid Metabolism: Carotenoids and Isoprenoids; Steroid Metabolism: Androgens and Estrogens; Carotenoids; Estrogens; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Rdh8 retinol dehydrogenase 8 71892412 Lipid Metabolism: Carotenoids and Isoprenoids; Steroid Metabolism: Androgens and Estrogens; Carotenoids; Estrogens; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Rdh9 retinol dehydrogenase 9 precursor 23680945 Lipid Metabolism: Carotenoids and Isoprenoids; Steroid Metabolism: Androgens and Estrogens; Carotenoids; Estrogens; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Renbp N-acylglucosamine 2-epimerase 257796315 Carbohydrate Metabolism: Amino Sugar Derivatives; Amino Sugars;
Rev3l DNA polymerase zeta catalytic subunit 1039732516 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Purines; Purine Metabolism;
Rexo1 RNA exonuclease 1 homolog* 34328282
Rexo2 oligoribonuclease, mitochondrial * 568958697
Rexo4 RNA exonuclease 4 * 568913428
Rfk riboflavin kinase* 14149726
Rnaseh1 ribonuclease H1 * 558516012
Rpa1 DNA-directed RNA polymerase I subunit RPA1 568975474 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Rpa2 DNA-directed RNA polymerase I subunit RPA2 110625961 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;
Rpe ribulose-phosphate 3-epimerase 568906790 Carbohydrates; Pentose Phosphate Pathways;
Rpe65 retinoid isomerohydrolase 568922139 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Rpia ribose-5-phosphate isomerase 94536844 Carbohydrate Metabolism: Pentoses and Pentose Cycle; Pentose Cycle; Carbohydrates; Pentose Phosphate Pathways;
Rrm1 ribonucleoside-diphosphate reductase large subunit 31982026 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Rrm2 ribonucleoside-diphosphate reductase subunit M2 7106399 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Rrm2b ribonucleoside-diphosphate reductase subunit M2 B 755550380 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Rsad1 radical S-adenosyl methionine domain-containing protein 1, mitochondrial * 755538526
Rsad2 radical S-adenosyl methionine domain-containing protein 2* 31543946
Rtn4ip1 reticulon-4-interacting protein 1, mitochondrial * 31543608
Sardh sarcosine dehydrogenase, mitochondrial 568913162 Lipid Metabolism: Glyco- and Phospholipids;
Sars2 serine--tRNA ligase, mitochondrial * 755520120
Sc5d lathosterol oxidase 568959341 Steroid Metabolism: Cholesterol Synthesis; Zoosterols;
Sccpdh saccharopine dehydrogenase-like oxidoreductase 30520019 Amino Acid Metabolism: Lysine; Lysine Metabolism; Amino Acids; Amino acids;
Scd acyl-CoA desaturase 2 13929208 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Scd1 acyl-CoA desaturase 1 31543675 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Scd2 acyl-CoA desaturase 2 188219606 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Scd3 stearoyl-coenzyme A desaturase 3 13277368 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Scd4 acyl-CoA desaturase 1 isoform X1 38261958 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Scd5 stearoyl-CoA desaturase 5 isoform b 148596938 Lipid Metabolism: Fatty Acids; Lipid Metabolism; Lipids; Lipid biosynthesis;
Scp2 non-specific lipid-transfer protein * 755507949
Sdha succinate dehydrogenase [ubiquinone] flavoprotein subunit, mitochondrial precursor 54607098 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Citrate and Glyoxalate Cycle; Glyoxylate Cycle; Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane; Hexoses; Glycolysis and TCA Cycle;
Sdhb succinate dehydrogenase [ubiquinone] iron-sulfur subunit, mitochondrial precursor 568931796 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Citrate and Glyoxalate Cycle; Glyoxylate Cycle; Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane; Hexoses; Glycolysis and TCA Cycle;
Sdr16c5 epidermal retinol dehydrogenase 2 32526863 Lipid Metabolism: Carotenoids and Isoprenoids; Carotenoids; Vitamins, Co-Enzymes, and Hormones; Isoprenoids; Isoprene Metabolism; Products of Isoprene Metabolism;
Sdr39u1 epimerase family protein SDR39U1* 131889222
Sds L-serine dehydratase/L-threonine deaminase 568937136 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Citrate and Glyoxalate Cycle; Lipid Metabolism: Glyco- and Phospholipids; Branched Chain Amino Acids; Glyoxylate Cycle; Sulfur Metabolism; Amino Acids; Carbohydrates; Amino acids; ATP Formation Spanning the Mitochondrial Inner Membrane; Glycolysis and TCA Cycle;
Sdsl serine dehydratase-like 1039771563 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Lipid Metabolism: Glyco- and Phospholipids; Branched Chain Amino Acids; Sulfur Metabolism; Amino Acids; Amino acids;
Seli ethanolaminephosphotransferase 1 207113155 Lipid Metabolism: Glyco- and Phospholipids; Phosphatides; Phospholipids;
Sephs1 selenide, water dikinase 1 1039758758 Lipid Metabolism: Carotenoids and Isoprenoids; Isoprenoids; Amino Acids; Amino acids;
Sephs2 selenophosphate synthetase 2 15011843 Lipid Metabolism: Carotenoids and Isoprenoids; Isoprenoids; Amino Acids; Amino acids;
Sgms1 phosphatidylcholine:ceramide cholinephosphotransferase 1 1039757412 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Sgms2 phosphatidylcholine:ceramide cholinephosphotransferase 2 27229211 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Shmt1 serine hydroxymethyltransferase, cytosolic 568972529 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; C1-Metabolism; One Carbon Pool; Sulfur Metabolism; Amino Acids; Amino acids; Folic Acid Metabolism; Folic Acid Reactions;
Shmt2 serine hydroxymethyltransferase, mitochondrial 356640163 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; C1-Metabolism; One Carbon Pool; Sulfur Metabolism; Amino Acids; Amino acids; Folic Acid Metabolism; Folic Acid Reactions;
Si sucrase-isomaltase, intestinal 6981536 Carbohydrates;
Sirt1 NAD-dependent protein deacetylase sirtuin-1 * 227430309
Sirt2 NAD-dependent protein deacetylase sirtuin-2 * 170650630
Sirt3 NAD-dependent protein deacetylase sirtuin-3 * 568952430
Sirt4 NAD-dependent protein lipoamidase sirtuin-4, mitochondrial * 1039772739
Sirt5 NAD-dependent protein deacylase sirtuin-5, mitochondrial * 755544814
Sirt6 NAD-dependent protein deacetylase sirtuin-6 * 755534814
Sirt7 NAD-dependent protein deacetylase sirtuin-7 * 1039736390
Smpd1 sphingomyelin phosphodiesterase 6755582 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Smpd2 sphingomyelin phosphodiesterase 2 1039732574 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Smpd3 sphingomyelin phosphodiesterase 3 755527089 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Smpd4 sphingomyelin phosphodiesterase 4 1039751946 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Smpd5 sphingomyelin phosphodiesterase 3-like isoform X3 568990915 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Sms spermine synthase 118600998 Amino Acids; Amino acids;
Soat1 sterol O-acyltransferase 1 84619697 Steroid Metabolism: Cholesterol Synthesis; Zoosterols;
Soat2 sterol O-acyltransferase 2 22122547 Steroid Metabolism: Cholesterol Synthesis; Zoosterols;
Sod1 superoxide dismutase [Cu-Zn]* 45597447
Sod2 superoxide dismutase [Mn], mitochondrial * 31980762
Sod3 extracellular superoxide dismutase [Cu-Zn] * 6755600
Sord sorbitol dehydrogenase 22128627 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Hexoses;
Spr sepiapterin reductase 160333789 Antibiotics: Penicillin, Cephalosporin; Pterine Biosynthesis;
Sptlc1 serine palmitoyltransferase 1 568982506 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Sptlc2 serine palmitoyltransferase 2 6755656 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Sptlc3 serine palmitoyltransferase 3 568916567 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Sqle squalene monooxygenase 6678127 Lipid Metabolism: Carotenoids and Isoprenoids; Isoprenoids;
Sqrdl sulfide:quinone oxidoreductase, mitochondrial * 568917957
Srd5a1 3-oxo-5-alpha-steroid 4-dehydrogenase 1 87044895 Isoprene Metabolism;
Srd5a2 3-oxo-5-alpha-steroid 4-dehydrogenase 2 16716485 Isoprene Metabolism;
Srd5a3 polyprenol reductase 27881427 Isoprene Metabolism;
Srm spermidine synthase 6678131 Amino Acids; Amino acids;
Srr serine racemase 1039737320 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Lipid Metabolism: Glyco- and Phospholipids; Sulfur Metabolism;
St6galnac1 alpha-N-acetylgalactosaminide alpha-2,6-sialyltransferase 1 precursor 126116572 Carbohydrates; Polysaccharides;
St6galnac2 alpha-N-acetylgalactosaminide alpha-2,6-sialyltransferase 2 31543707 Carbohydrates; Polysaccharides;
St6galnac3 alpha-N-acetylgalactosaminide alpha-2,6-sialyltransferase 3 755503560 Carbohydrates; Polysaccharides;
St6galnac4 alpha-N-acetyl-neuraminyl-2,3-beta-galactosyl-1, 3-N-acetyl-galactosaminide alpha-2,6-sialyltransferase isoform X3 449083362 Carbohydrates; Polysaccharides;
St6galnac5 sialyltransferase 7E 148540137 Carbohydrates; Polysaccharides;
St6galnac6 ST6 (alpha-N-acetyl-neuraminyl-2,3-beta-galactosyl-1, 3)-N-acetylgalactosaminide alpha-2,6-sialyltransferase 6 575501651 Carbohydrates; Polysaccharides;
Steap1 metalloreductase STEAP1 254553462 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
Steap2 metalloreductase STEAP2 550822361 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
Steap3 metalloreductase STEAP3 146134512 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
Steap4 metalloreductase STEAP4 31981509 Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments;
Sts steryl-sulfatase precursor 6678175 Steroid Metabolism: Androgens and Estrogens; Androgens;
Sucla2 succinate--CoA ligase [ADP-forming] subunit beta, mitochondrial * 46849708
Suclg1 succinyl-CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial precursor 255958286 Citrate and Glyoxalate Cycle; Glyoxylate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle;
Suclg2 succinyl-CoA ligase [GDP-forming] subunit beta, mitochondrial 1030311308 Citrate and Glyoxalate Cycle; Glyoxylate Cycle; Carbohydrates; TCA Cycle in the Mitochondrial Matrix; Glycolysis and TCA Cycle;
Sugct succinate--hydroxymethylglutarate CoA-transferase * 755544156
Sult1a1 sulfotransferase 1A1 1039777790 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Estrogens; Sulfur Metabolism;
Sult1a2 sulfotransferase 1A2 29550893 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Estrogens; Sulfur Metabolism;
Sult1a3 sulfotransferase 1A3/1A4 29550921 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Estrogens; Sulfur Metabolism;
Sult1a4 sulfotransferase 1A3/1A4 62868225 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Estrogens; Sulfur Metabolism;
Sult1b1 sulfotransferase family cytosolic 1B member 1 568936071 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Estrogens; Sulfur Metabolism;
Sult1c1 sulfotransferase 1C1 40254554 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Estrogens; Sulfur Metabolism;
Sult1c2 sulfotransferase 1C2 34328501 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Estrogens; Sulfur Metabolism;
Sult1c3 sulfotransferase 1C1 148747248 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Estrogens; Sulfur Metabolism;
Sult1c4 sulfotransferase 1C4 isoform X1 1012443738 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Estrogens; Sulfur Metabolism;
Sult1d1 sulfotransferase 1 family member D1 188219649 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Estrogens; Sulfur Metabolism;
Sult1e1 estrogen sulfotransferase 256985138 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Estrogens; Sulfur Metabolism;
Sult2a1 bile salt sulfotransferase 162329581 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Sulfur Metabolism;
Sult2a2 alcohol sulfotransferase 296923707 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Sulfur Metabolism;
Sult2a3 sulfotransferase family 2A member 1 family member 357197126 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Sulfur Metabolism;
Sult2a4 sulfotransferase family member-like 568946135 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Sulfur Metabolism;
Sult2a5 sulfotransferase family 2A member 1 family member 297139699 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Sulfur Metabolism;
Sult2a6 alcohol sulfotransferase A 568946365 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Sulfur Metabolism;
Sult2a7 sulfotransferase family 2A member 1 family member 296923713 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Sulfur Metabolism;
Sult2b1 sulfotransferase family cytosolic 2B member 1 229092371 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Steroid Metabolism: Androgens and Estrogens; Androgens; Sulfur Metabolism;
Suox sulfite oxidase, mitochondrial precursor 74024924 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Taldo1 transaldolase 33859640 Carbohydrate Metabolism: Pentoses and Pentose Cycle; Pentose Cycle; Carbohydrates; Pentose Phosphate Pathways;
Tars threonine--tRNA ligase, cytoplasmic* 27229277
Tars2 threonine--tRNA ligase, mitochondrial * 1039765102
Tat tyrosine aminotransferase 22122769 Amino Acid Metabolism: Histidine; Histidine Metabolism; Amino Acids; Aromatic amino acids;
Tbxas1 thromboxane-A synthase 1039774702 Lipids; Lipid biosynthesis; Prostaglandins, Thromboxanes, and Leucotrienes;
Tdh L-threonine 3-dehydrogenase, mitochondrial 254281204 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Tdo2 tryptophan 2,3-dioxygenase 31982697 Nucleotide Metabolism: NAD, NADP; Amino Acids; Aromatic amino acids;
Tfb1m dimethyladenosine transferase 1, mitochondrial * 568997984
Tfb2m dimethyladenosine transferase 2, mitochondrial isoform 3* 1061975067
Tgds dTDP-D-glucose 4,6-dehydratase 225579052 Carbohydrates; Polysaccharides;
Th tyrosine 3-monooxygenase 6678337 Amino Acid Metabolism: Histidine; Histidine Metabolism; Vitamins, Co-Enzymes, and Hormones; Catecholamines;
Them4 acyl-coenzyme A thioesterase THEM4* 110626050
Them5 acyl-coenzyme A thioesterase THEM5* 21539589
Them6 protein THEM6 * 38348460
Them7 uncharacterized protein LOC74088 * 755500674
Thg1l probable tRNA(His) guanylyltransferase * 755539368
Tk1 thymidine kinase, cytosolic 568973591 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Pyrimidine Metabolism;
Tk2 thymidine kinase 2, mitochondrial 1039790429 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Pyrimidine Metabolism;
Tkt transketolase* 6678359
Tktl1 transketolase-like protein 1 125347421 Carbohydrate Metabolism: Pentoses and Pentose Cycle; Pentose Cycle; Carbohydrates; Pentose Phosphate Pathways;
Tktl2 transketolase-like 2 isoform X1 409191601 Carbohydrate Metabolism: Pentoses and Pentose Cycle; Pentose Cycle; Carbohydrates; Pentose Phosphate Pathways;
Tmlhe trimethyllysine dioxygenase, mitochondrial 569016299 Amino Acids; Amino acids;
Tomt transmembrane O-methyltransferase 530719562 Vitamins, Co-Enzymes, and Hormones; Catecholamines;
Tph1 tryptophan 5-hydroxylase 1 444909167 Amino Acid Metabolism: Histidine; Histidine Metabolism; Amino Acids; Aromatic amino acids;
Tph2 tryptophan 5-hydroxylase 2 148540044 Amino Acid Metabolism: Histidine; Histidine Metabolism; Amino Acids; Aromatic amino acids;
Tpi1 triosephosphate isomerase 226958349 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Pentose Phosphate Pathways;
Tpo thyroid peroxidase precursor 755541300 Amino Acid Metabolism: Histidine; Histidine Metabolism;
Trit1 tRNA dimethylallyltransferase, mitochondrial * 1039768452
Trmt1 tRNA (guanine(26)-N(2))-dimethyltransferase * 1039787872
Trmt10c mitochondrial ribonuclease P protein 1 * 21312876
Trmt11 tRNA (guanine(10)-N2)-methyltransferase homolog * 755533256
Trmt12 tRNA wybutosine-synthesizing protein 2 homolog* 118150645
Trmt13 tRNA:m(4)X modification enzyme TRM13 homolog * 1039764287
Trmt2a tRNA (uracil-5-)-methyltransferase homolog A * 1039750612
Trmt2b tRNA (uracil(54)-C(5))-methyltransferase homolog * 755566158
Trmt5 tRNA (guanine(37)-N1)-methyltransferase * 1039742113
Trmt6 tRNA (adenine(58)-N(1))-methyltransferase non-catalytic subunit TRM6* 148747333
Trmu mitochondrial tRNA-specific 2-thiouridylase 1 * 568993393
Trnt1 CCA tRNA nucleotidyltransferase 1, mitochondrial * 568942819
Trub1 probable tRNA pseudouridine synthase 1 * 755563672
Trub2 probable tRNA pseudouridine synthase 2 * 568913452
Tst thiosulfate sulfurtransferase 6678449 Amino Acid Metabolism: Serine, Threonine, Cysteine, Methionine; Sulfur Metabolism;
Txndc11 thioredoxin domain-containing protein 11 * 1039750378
Txndc12 thioredoxin domain-containing protein 12 * 13384700
Txndc15 thioredoxin domain-containing protein 15 * 52693935
Txndc16 thioredoxin domain-containing protein 16 * 1039746845
Txndc17 thioredoxin domain-containing protein 17* 13386060
Txndc2 thioredoxin domain-containing protein 2 * 225579134
Txndc5 thioredoxin domain-containing protein 5 isoform 3* 575771915
Txndc8 thioredoxin domain-containing protein 8 * 568927270
Txndc9 thioredoxin domain-containing protein 9* 25286717
Txnrd1 thioredoxin reductase 1, cytoplasmic 110224445 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purine Metabolism; Pyrimidine Metabolism;
Txnrd2 thioredoxin reductase 2, mitochondrial precursor 102468565 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purine Metabolism; Pyrimidine Metabolism;
Txnrd3 thioredoxin reductase 3 isoform 1 296010807 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purine Metabolism; Pyrimidine Metabolism;
Tymp thymidine phosphorylase 19923857 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Pyrimidines; Pyrimidine Metabolism;
Tyms thymidylate synthase 46358062 Nucleotide Metabolism: Pyrimidines; Pyrimidines; Purines and Pyrimidines; Pyrimidines; Folic Acid Metabolism; Folic Acid Reactions; Pyrimidine Metabolism;
Tyr tyrosinase precursor 568950109 Vitamins, Co-Enzymes, and Hormones; Catecholamines;
Uap1 UDP-N-acetylhexosamine pyrophosphorylase 1039727254 Carbohydrate Metabolism: Amino Sugar Derivatives; Carbohydrates; Polysaccharides;
Uck1 uridine-cytidine kinase 1 568913295 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Uck1l uridine-cytidine kinase-like 1 isoform 2 301129207 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Uck2 uridine-cytidine kinase 2 1039730414 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Uckl1 uridine-cytidine kinase-like 1 1039761820 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism; Pyrimidine Metabolism;
Ugdh UDP-glucose 6-dehydrogenase 568934033 Carbohydrate Metabolism: Di-and Polysaccharides; Carbohydrates; Polysaccharides;
Ugp2 UTP--glucose-1-phosphate uridylyltransferase 594591591 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Polysaccharides;
Ugt1a1 UDP-glucuronosyltransferase 1-1 precursor 145699099 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt1a10 UDP glycosyltransferase 1 family, polypeptide A10 precursor 145864477 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt1a2 UDP-glucuronosyltransferase 1-2 precursor 32526871 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt1a3 UDP-glucuronosyltransferase 1-3 precursor 66773200 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt1a4 UDP-glucuronosyltransferase 1-4 precursor 6005930 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt1a5 UDP-glucuronosyltransferase 1-5 precursor 145699137 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt1a6 UDP-glucuronosyltransferase 1-6 precursor 89276780 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt1a7c UDP-glucuronosyltransferase 1-7 precursor 47059123 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt1a8 UDP-glucuronosyltransferase 1-8 precursor 89276785 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt1a9 UDP glycosyltransferase 1 family, polypeptide A10 precursor 145864463 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2a1 UDP-glucuronosyltransferase 2A1 precursor 158937326 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2a2 UDP-glucuronosyltransferase 2A2 precursor 66571303 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2a3 UDP-glucuronosyltransferase 2A3 precursor 254587896 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2b UDP-glucuronosyltransferase 2B2 precursor 402478642 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2b1 UDP-glucuronosyltransferase 2B1 precursor 22779901 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2b10 UDP-glucuronosyltransferase 2B10 precursor 300794198 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2b11 UDP-glucuronosyltransferase 2B11 precursor 4507823 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2b15 UDP-glucuronosyltransferase 2B15 precursor 51948510 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2b17 UDP-glucuronosyltransferase 2B17 precursor 31543923 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2b28 UDP-glucuronosyltransferase 2B28 isoform 1 precursor 16596680 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2b37 UDP-glucuronosyltransferase 2B37 precursor 27753955 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2b4 UDP-glucuronosyltransferase 2B4 isoform 2 precursor 662236745 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2b5 UDP-glucuronosyltransferase 2B17 precursor 306518591 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt2b7 UDP-glucuronosyltransferase 2B7 precursor 27545412 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt3a1 UDP-glucuronosyltransferase 3A1 precursor 164450477 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt3a2 UDP-glucuronosyltransferase 3A2-like 21450243 Carbohydrate Metabolism: Acidic Carbohydrate Derivatives; Steroid Metabolism: Androgens and Estrogens; Tetrapyrrole Metabolism: Heme, Cytochromes, Cholorphyll; Bile Pigments; Estrogens; Carbohydrates; Polysaccharides;
Ugt8 2-hydroxyacylsphingosine 1-beta-galactosyltransferase precursor 9507235 Lipid Metabolism: Sphingolipids; Lipids; Phospholipids;
Umps uridine 5'-monophosphate synthase 568995073 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Pyrimidines; Pyrimidine Metabolism;
Ung uracil-DNA glycosylase * 568937107
Uox uricase 6678509 Nucleotide Metabolism: Purines; Purines and Pyrimidines; Purines; Purine Metabolism;
Upb1 beta-ureidopropionase 19527212 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidines; Purines and Pyrimidines; Pyrimidines; Pyrimidine Metabolism;
Upp1 uridine phosphorylase 1 568970183 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Upp2 uridine phosphorylase 2 1039762263 Nucleotide Metabolism: Pyrimidines; Pyrimidine Biosynthesis; Pyrimidine Metabolism;
Uqcrb ubiquinol-cytochrome c reductase complex 14 kDa protein 13385726 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Uqcrc1 ubiquinol-cytochrome-c reductase complex core protein 1 46593021 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Uqcrc2 ubiquinol-cytochrome-c reductase complex core protein 2 22267442 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Uqcrfs1 ubiquinol-cytochrome c reductase 8 kDa protein 13385168 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Uqcrh ubiquinol-cytochrome c reductase complex 11 kDa protein 21539599 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Uqcrq ubiquinol-cytochrome c reductase complex 9.5 kDa protein 1031698715 Carbohydrates; ATP Formation Spanning the Mitochondrial Inner Membrane;
Uroc1 urocanate hydratase-like 568941805 Amino Acid Metabolism: Histidine; Histidine Metabolism; Amino Acids; Amino acids;
Urod uroporphyrinogen decarboxylase 568928764 Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Porphyrins; Vitamins, Co-Enzymes, and Hormones; Porphyrins; Heme Metabolism;
Uros uroporphyrinogen-III synthase 690969217 Tetrapyrrole Metabolism: Porphyrins, Cobalamin; Porphyrins; Vitamins, Co-Enzymes, and Hormones; Porphyrins; Heme Metabolism;
Vars valine--tRNA ligase 1039753239 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids;
Vars2 valine--tRNA ligase, mitochondrial precursor 755558902 Amino Acid Metabolism: Leucine, Isoleucine, Valine; Branched Chain Amino Acids;
Vps29 vacuolar protein sorting-associated protein 29 568937407 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Lipid Metabolism: Fatty Acids; Lipid Metabolism; Amino Acids; Lipids; Amino acids; Lipid biosynthesis; Lipid Metabolism;
Vps4a vacuolar protein sorting-associated protein 4A 18699726 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Glycolysis and TCA Cycle;
Vps4b vacuolar protein sorting-associated protein 4B 164698506 Carbohydrate Metabolism: Glycolysis and Gluconeogenesis; Carbohydrates; Glycolysis in the Cytoplasm; Gluconeogenesis and Glycolysis; Glycolysis and TCA Cycle;
Wars2 tryptophan--tRNA ligase, mitochondrial * 1039765026
Wrnip1 ATPase WRNIP1 254540120 Nucleotide Metabolism: Purines;
Xdh xanthine dehydrogenase/oxidase 77682555 Nucleotide Metabolism: Purines; Purines and Pyrimidines; Purines; Purine Metabolism;
Xylb xylulose kinase 1039791824 Carbohydrate Metabolism: Pentoses and Pentose Cycle; Pentose Interconversions; Carbohydrates; Pentoses; Purine Metabolism;
Yars2 tyrosine--tRNA ligase, mitochondrial* 39930579
Zadh2 zinc-binding alcohol dehydrogenase domain-containing protein 2 * 569005295
Znrd1 DNA-directed RNA polymerase I subunit RPA12 569001355 Nucleotide Metabolism: Purines; Nucleotide Metabolism: Pyrimidines; Purines; Pyrimidine Biosynthesis; Purines and Pyrimidines; Purines; Pyrimidines; Purine Metabolism;

*Added from MitoCarta Database